
Muchas afecciones cutáneas afectan al sistema tegumentario humano , el sistema de órganos que cubre toda la superficie del cuerpo y está compuesto por piel , pelo , uñas y músculos y glándulas relacionados . [ 1 ] La función principal de este sistema es la de barrera contra el entorno externo. [ 2 ] La piel pesa un promedio de cuatro kilogramos, cubre un área de dos metros cuadrados y está formada por tres capas distintas: la epidermis , la dermis y el tejido subcutáneo . [ 1 ] Los dos tipos principales de piel humana son: la piel glabra , la piel sin pelo de las palmas y las plantas de los pies (también denominada superficie "palmoplantar"), y la piel con pelo. [ 3 ] Dentro de este último tipo, los pelos se encuentran en estructuras llamadas unidades pilosebáceas , cada una con folículo piloso , glándula sebácea y músculo erector del pelo asociado . [ 4 ] En el embrión , la epidermis, el pelo y las glándulas se forman a partir del ectodermo , que está químicamente influenciado por el mesodermo subyacente que forma la dermis y los tejidos subcutáneos. [ 5 ] [ 6 ] [ 7 ]
La epidermis es la capa más superficial de la piel, un epitelio escamoso con varios estratos : el estrato córneo , el estrato lúcido , el estrato granuloso , el estrato espinoso y el estrato basal . [ 8 ] La nutrición de estas capas se proporciona por difusión desde la dermis ya que la epidermis no tiene irrigación sanguínea directa. La epidermis contiene cuatro tipos de células: queratinocitos , melanocitos , células de Langerhans y células de Merkel . De estas, los queratinocitos son el componente principal, constituyendo aproximadamente el 95 por ciento de la epidermis. [ 3 ] Este epitelio escamoso estratificado se mantiene por división celular dentro del estrato basal, en el que las células diferenciadas se desplazan lentamente hacia afuera a través del estrato espinoso hasta el estrato córneo, donde las células se desprenden continuamente de la superficie. [ 3 ] En la piel normal, la tasa de producción es igual a la tasa de pérdida; Se necesitan aproximadamente dos semanas para que una célula migre desde la capa de células basales hasta la parte superior de la capa de células granulares, y otras dos semanas para cruzar el estrato córneo. [ 9 ]
La dermis es la capa de piel entre la epidermis y el tejido subcutáneo, y comprende dos secciones, la dermis papilar y la dermis reticular . [ 10 ] La dermis papilar superficial se interdigita con las crestas de la rete suprayacentes de la epidermis, entre las cuales las dos capas interactúan a través de la zona de la membrana basal. [ 10 ] Los componentes estructurales de la dermis son el colágeno , las fibras elásticas y la sustancia fundamental . [ 10 ] Dentro de estos componentes se encuentran las unidades pilosebáceas, los músculos erectores del pelo y las glándulas ecrinas y apocrinas . [ 8 ] La dermis contiene dos redes vasculares que corren paralelas a la superficie de la piel —un plexo superficial y un plexo profundo— que están conectados por vasos comunicantes verticales. [ 8 ] [ 11 ] La función de los vasos sanguíneos dentro de la dermis es cuádruple: suministrar nutrientes, regular la temperatura, modular la inflamación y participar en la cicatrización de heridas. [ 12 ] [ 13 ]
El tejido subcutáneo es una capa de grasa entre la dermis y la fascia subyacente . [ 14 ] Este tejido se puede dividir a su vez en dos componentes: la capa grasa propiamente dicha, o panículo adiposo , y una capa muscular vestigial más profunda, el panículo carnoso . [ 3 ] El principal componente celular de este tejido es el adipocito , o célula grasa. [ 14 ] La estructura de este tejido está compuesta por compartimentos septales (es decir, hebras lineales) y lobulares , que difieren en su aspecto microscópico. [ 8 ] Funcionalmente, la grasa subcutánea aísla el cuerpo, absorbe los traumatismos y sirve como fuente de energía de reserva. [ 14 ]
Las afecciones del sistema tegumentario humano constituyen un amplio espectro de enfermedades, también conocidas como dermatosis , así como muchos estados no patológicos (como, en ciertas circunstancias, la melanoniquia y las uñas de raqueta ). [ 15 ] [ 16 ] Si bien solo un pequeño número de enfermedades de la piel representan la mayoría de las visitas al médico , se han descrito miles de afecciones de la piel. [ 14 ] La clasificación de estas afecciones a menudo presenta muchos desafíos nosológicos , ya que las etiologías y patogenias subyacentes a menudo no se conocen. [ 17 ] [ 18 ] Por lo tanto, la mayoría de los libros de texto actuales presentan una clasificación basada en la ubicación (por ejemplo, afecciones de la membrana mucosa ), morfología ( afecciones ampollosas crónicas ), etiología ( afecciones de la piel resultantes de factores físicos ), etc. [ 19 ] [ 20 ] Clínicamente, el diagnóstico de cualquier afección cutánea particular se realiza recopilando información pertinente sobre la (s) lesión(es) cutánea (s) que se presenta(n), incluyendo la ubicación (como brazos, cabeza, piernas), síntomas ( prurito , dolor), duración (aguda o crónica), disposición (solitaria, generalizada, anular, lineal), morfología ( máculas , pápulas , vesículas ) y color (rojo, azul, marrón, negro, blanco, amarillo). [ 21 ] El diagnóstico de muchas afecciones a menudo también requiere una biopsia de piel que proporciona información histológica [ 22 ] [ 23 ] que puede correlacionarse con la presentación clínica y cualquier dato de laboratorio. [ 24 ] [ 25 ] [ 26 ]
Erupciones acneiformes


Las erupciones acneiformes son causadas por cambios en la unidad pilosebácea . [ 27 ] [ 28 ]
- Acne aestivalis (acné de Mallorca) [ nb 1 ] [ nb 2 ] [ nb 3 ]
- Acné conglobata
- Acne cosmetica (acné cosmético)
- Acné fulminante (acné ulcerativo febril agudo)
- Acné queloideo nucal (acné queloideo, dermatitis papilar del cuero cabelludo, foliculitis queloideo, foliculitis queloideo nucal, acné queloideo nucal)
- Acné mecánico
- Acné medicamentosa
- Acné miliar necrótico (acné varioliforme)
- Acné vulgar (acné simple)
- Acné con edema facial (edema facial sólido) [ nb 4 ]
- Blefarofima
- Cloracné
- Rosácea eritrotelangiectásica (rosácea eritematotelangiectásica, rosácea vascular)
- Acné excoriado ( acné excoriée des jeunes filles , acné de Picker) [ nb 5 ]
- Rosácea glandular
- Gnatofima
- rosácea gramnegativa
- Dermatitis facial granulomatosa
- Dermatitis perioral granulomatosa
- acné halógeno
- Hidradenitis supurativa (acné inverso, pioderma fístula significativa, enfermedad de Verneuil)
- Granuloma facial aséptico idiopático
- acné infantil
- Rosácea lupoide (rosácea granulomatosa, tuberculide micropapular, tuberculide de Lewandowsky similar a la rosácea)
- Lupus miliaris diseminado faciei
- Metofima
- Acné neonatal (acné infantil, acné neonatorum, pustulosis cefálica neonatal)
- acné ocupacional
- Acné graso
- Rosácea ocular (rosácea oftálmica, oftalmorosácea)
- Otofima
- Dermatitis periorificial
- Edema persistente de rosácea (edema eritematoso crónico de la parte superior del rostro, enfermedad de Morbihan, linfedema rosáceo)
- Rosácea fimatosa
- Pomada para el acné
- Rosácea papulopustulosa (rosácea inflamatoria)
- Perifoliculitis capitis abscedens et suffodiens (celulitis disecante del cuero cabelludo, foliculitis disecante, perifoliculitis capitis abscedens et suffodiens de Hoffman)
- Dermatitis perioral
- Dermatitis periorbitaria (dermatitis periocular)
- Pioderma facial (rosácea fulminante)
- Rinofima
- Rosácea (acné rosácea)
- Rosácea conglobata
- Síndrome de sinovitis-acné-pustulosis-hiperostosis-osteomielitis (síndrome SAPHO) [ nb 6 ]
- rosácea esteroidea
- acné de alquitrán
- acné tropical
síndromes autoinflamatorios
Los síndromes autoinflamatorios son un grupo de trastornos hereditarios caracterizados por episodios de lesiones cutáneas inflamatorias y fiebres periódicas . [ 29 ] [ 30 ]
- síndrome de Blau

síndrome de Blau - síndrome neurológico, cutáneo y articular infantil crónico
- Urticaria por frío familiar (síndrome autoinflamatorio por frío familiar)
- Fiebre mediterránea familiar
- Síndrome de hiper-IgD [ nb 7 ]
- Síndrome de Majeed
- Síndrome de Muckle-Wells
- síndrome periódico asociado al receptor del TNF (fiebre hiberniana familiar, TRAPS, síndrome periódico asociado al receptor del factor de necrosis tumoral)
Ampollas crónicas
Las afecciones cutáneas ampollosas crónicas tienen un curso prolongado y se presentan con vesículas y ampollas . [ 31 ] [ 32 ] [ 33 ]
- enfermedad lineal por IgA en adultos
- Penfigoide ampolloso
- lupus eritematoso ampolloso
- Enfermedad lineal por IgA infantil (enfermedad ampollosa crónica de la infancia)
- Penfigoide cicatricial (penfigoide mucoso benigno, penfigoide de la membrana mucosa benigno, pénfigo ocular, penfigoide cicatricial)
- Dermatitis herpetiforme (enfermedad de Duhring)
- Dishidrosis (dermatitis vesicular palmoplantar recurrente, eccema vesiculobulloso agudo de las manos, dermatitis dishidrótica, pomfolix)
- Pénfigo endémico (pénfigo foliáceo endémico, fogo selvagem)
- Epidermólisis ampollosa adquirida
- Enfermedad de Grover (dermatosis acantolítica papular benigna, dermatosis acantolítica persistente, dermatosis acantolítica transitoria)
enfermedad de Grover - pénfigo por IgA
- Dermatosis intraepidérmica neutrofílica por IgA
- Penfigoide cicatricial localizado (penfigoide cicatricial de Brunsting-Perry)
- pénfigo paraneoplásico
- Pénfigo eritematoso (síndrome de Senear-Usher)
- Pénfigo foliáceo
- Pénfigo herpetiforme (dermatitis herpetiforme acantolítica, pénfigo herpetiforme, enfermedad ampollosa mixta, pénfigo controlado con sulfapiridina)
- Penfigoide nodular
- Pénfigo vegetante
- Pénfigo vegetante de Hallopeau
- Pénfigo vegetante de Neumann
- Pénfigo vulgar
- Penfigoide vesicular
- penfigoide infantil vulvar
Condiciones de las membranas mucosas
Las afecciones de las membranas mucosas incluyen los revestimientos húmedos de los ojos, la nariz, la boca, los genitales y el ano. [ 34 ]
- Acatalasia (acatalasemia, enfermedad de Takahara)
- Leucoplasia disqueratósica adquirida
- Queilitis actínica (queilosis actínica)
- Gingivitis ulcerativa necrosante aguda (gingivitis membranosa aguda, gingivoestomatitis ulcerativa necrosante aguda, gingivitis fusoespirilar, fusoespirilosis, gingivitis fusospiroquetal, gingivitis necrosante, gingivitis fagedénica, boca de trinchera, gingivitis ulcerativa, gingivitis de Vincent, infección de Vincent, estomatitis de Vincent, enfermedad de Vincent)
- queilitis alérgica de contacto
- Angina bullosa hemorrágica
- Queilitis angular ( perlèche )
- Enfermedad de Behçet (síndrome de Behçet, síndrome óculo-oral-genital)
- Lengua negra vellosa (lingua villosa nigra)

Lengua negra peluda - Lengua de caviar
- Queilitis exfoliativa
- Queilitis glandular
- Queilitis granulomatosa (queilitis granulomatosa, granulomatosis orofacial)
- Seno cutáneo de origen dental (seno dental)
- Neutropenia cíclica
- gingivitis descamativa
- Úlcera labial inducida por fármacos
- Epidermización del labio
- Epulis
- Épulis fisuratum (granuloma fisuratum)
- papilitis lingual eruptiva
- Eritroplasia (eritroplasia)
- Lengua fisurada (lengua surcada, lengua plicata, lengua plicada, lengua escrotal)
- Lengua geográfica (glositis migratoria benigna, estomatitis migratoria benigna, glositis areata exfoliativa, glositis areata migrans, lingua geographica, estomatitis areata migrans, placas benignas transitorias de la lengua)
- fibroma gingival
- Hipertrofia gingival
- Leucoplasia vellosa (leucoplasia vellosa oral)
- seno dental intraoral
- Línea alba
- Leucoplasia
- Leucoplasia con tilosis y carcinoma esofágico
- Úlcera aftosa mayor (periadenitis mucosa necrótica recurrente)
- Glositis romboidal media (atrofia papilar central)
- lesión oral melanocítica
- Síndrome de Melkersson-Rosenthal
- Morsicatio buccarum (mordedura crónica de mejilla, masticación crónica de mejilla)
- Carcinoma de células escamosas de la mucosa
- Quiste mucoso de la mucosa oral (mucocele)
- Lugares de Nagayama
- Enfermedad de Crohn oral
- papilomatosis oral florida
- melanosis oral
- coristoma óseo de la lengua
- Ameloblastoma periférico
- Queilitis de células plasmáticas (gingivitis de células plasmáticas, mucositis orificial de células plasmáticas)
- Plasmoacantoma
- leucoplasia verrugosa proliferativa
- Granuloma piógeno (hemangioma eruptivo, hemangioma de tejido de granulación, granuloma gravídico, hemangioma capilar lobular, tumor del embarazo, tumor del embarazo)

Granuloma piógeno - Piostomatitis vegetante
- Estomatitis aftosa recurrente (aftas, úlceras bucales, aftas orales recurrentes)
- Infección recurrente por herpes simple intraoral
- Lengua lisa (glositis atrófica, lengua calva, glositis de Hunter, lengua de Moeller)
- Estomatitis nicotínica (estomatitis por nicotina, queratosis del fumador, manchas del fumador)
- Torus palatino
- Verruga del trompetero
- papilomatosis vestibular
- Nevo esponjoso blanco (nevo esponjoso blanco de Cannon)
Condiciones de los apéndices cutáneos
Las afecciones de los anexos cutáneos son aquellas que afectan a las glándulas de la piel, el pelo , las uñas y los músculos erectores del pelo . [ 1 ] [ 35 ]
- Acné necrótico
- Hipertricosis generalizada adquirida (hipertricosis lanuginosa adquirida, hipertricosis lanuginosa acquisita)
- Dermatosis perforante adquirida (colagenosis perforante adquirida)
- Acroqueratosis paraneoplásica de Bazex (acroqueratosis neoplásica, síndrome de Bazex)
- Acroosteólisis
- Paroniquia aguda
- Alopecia areata
Alopecia areata - Alopecia neoplásica
- efluvio anágeno
- alopecia androgénica (alopecia androgenética)
- Anhidrosis (hipohidrosis)
- Anoniquia
- Leuconiquia aparente
- Las líneas de Beau
- Uñas azules
- Bromidrosis (bromhidrosis apocrina, sudor fétido, sudoración maloliente, osmidrosis)
- deformidad del cabello burbuja
- Alopecia cicatricial centrífuga central (síndrome de degeneración folicular, pseudopelada del cuero cabelludo central)
- Clavo en espiga (clavo de chevrón)
- Cromhidrosis (sudoración coloreada)
- paroniquia crónica
- alopecia cicatricial
- Aporreo (dedos de baqueta, dedos hipocráticos, uñas de cristal de reloj)
- Onicodisplasia congénita de los dedos índices
- Infundibulofoliculitis diseminada y recurrente
- Dermatitis pustulosa erosiva del cuero cabelludo (dermatosis pustulosa erosiva del cuero cabelludo)
- Eritromelanosis folicular faciei y coli
- Foliculitis decalvante
- Foliculitis de las narinas perforantes
- Enfermedad de Fox-Fordyce
- Alopecia frontal fibrosante
- Hipertricosis congénita generalizada (hipertricosis lanuginosa congénita)
- Hiperhidrosis generalizada
- Síndrome de Graham-Little
- Granulosis rubra nasi
- uñas verdes
- Hiperhidrosis gustativa
- Moldes capilares (seudonites)
- Nevo del folículo piloso (vello hamartoma)
- Palmas y plantas de los pies peludas
- Uñas mitad y mitad (las uñas de Lindsay)
- Padrastro
- Hapalonychia
- Hematidrosis
- Hirsutismo
- Clavo de gancho
- alopecia con peine caliente
- Hipertricosis cubital (síndrome del codo peludo)
- Hipertricosis simple del cuero cabelludo
- Distrofia intermitente del folículo piloso
- Queratosis pilaris atrófica
- Cabello rizado (rizo progresivo adquirido)
- Tumor de Koenen (fibroma periungueal de Koenen, fibroma periungueal)
- Coiloniquia (uñas en forma de cuchara)
- Enfermedad de Kyrle
- Leuconiquia (uñas blancas)
- Liquen planopilar (acuminatus, liquen plano folicular, liquen plano folicular, peripilar)
- Liquen plano de las uñas
- Liquen espinuloso (queratosis espinulosa)
- Alopecia lipedematosa (cuero cabelludo lipedematoso)
- Hipertricosis adquirida localizada
- Hipertricosis congénita localizada
- eritroniquia longitudinal
- melanoniquia longitudinal
- Síndrome de cabello anágeno suelto (síndrome del cabello anágeno suelto)
- Lupus eritematoso
- Madarosis
- Desalineación de la placa ungueal
- Calvicie de patrón masculino
- Hipotricosis hereditaria de Marie-Unna (hipotricosis de Marie-Unna)
- Distrofia ungueal mediana (distrofia ungueal mediana canaliforme, distrofia canaliforme mediana de Heller, solenoniquia)
- Las líneas de Mees
- Melanoniqia
- Síndrome del cabello rizado de Menkes (enfermedad del cabello rizado, enfermedad de Menkes)
- Moniletrix (cabello con cuentas)
- Las uñas de Muehrcke (Las líneas de Muehrcke)
- Síndrome de uña-rótula (síndrome de Fong, osteoonicodisplasia hereditaria, síndrome HOOD)

Síndrome de uña-rótula - Neoplasias del lecho ungueal
- Hipertricosis nevoide
- alopecia no cicatricial
- Onicauxis
- Onicoatrofia
- Onicocriptosis (uña encarnada, unguis incarnatus)
- Onicogrifosis (uñas con forma de cuerno de carnero)
- Onicólisis
- Onicomadesis
- Onicomatricoma
- Onicofagia (morderse las uñas)
- Onicofosis
- Onicoptosis defluvio (alopecia unguium)
- Onicorrexis (uñas quebradizas)
- Onicosquisis
- Onicotilomanía

Onicotilomanía - Ofiasis
- Hiperhidrosis palmoplantar (hiperhidrosis emocional)
- Paraqueratosis pustulosa
- Hipertricosis adquirida con patrón
- foliculitis perforante
- Pili annulati (cabello anillado)
- Pili bifurcati
- Pili multigéminis
- Pili pseudoannulati (pseudo pili annulati)
- Pili torti (cabellos retorcidos)
- Uñas en pinza (uñas omega, uñas trompeta)
- Pitiriasis amiantácea (tinea amiantácea)
- Platonychia
- Plica neuropathica (pelo afieltrado)
- Clavo del fontanero
- Encanecimiento prematuro del cabello
- Hipertricosis prepuberal
- Alopecia por presión (alopecia postoperatoria, alopecia inducida por presión)
- Pseudofoliculitis de la barba (picazón del barbero, foliculitis de la barba traumática, protuberancias por afeitado, pseudofoliculitis cicatricial de la barba, protuberancias por afeitado)
- Pseudopelada de Brocq (alopecia cicatrisata)
- Uñas psoriásicas
- Pterigión inversum unguis (pterigión inversus unguis, pterigión ventral)
- Pterigión unguis (pterigión dorsal)
- Púrpura del lecho ungueal
- Uña de raqueta (braquioniquia, uña en raqueta , pulgar de raqueta)
- Hidradenitis palmoplantar recurrente (hidradenitis palmoplantar idiopática, hidradenitis plantar idiopática, eritema plantar doloroso, hidradenitis ecrina palmoplantar, paniculitis plantar)
- lúnulas rojas
- Síndrome de Ross
- Síndrome de Rubinstein-Taybi
- Síndrome de Setleis
- síndrome de uñas de concha
- síndrome anágeno corto
- hemorragia por astilla

hemorragia por astilla - lúnulas moteadas
- Manchas en la placa ungueal
- Hematoma subungueal
- efluvio telógeno
- Las uñas de Terry
- alopecia por tracción
- Alopecia traumática
- Foliculosis anserina traumática
- Alopecia triangular (alopecia temporal, alopecia triangular temporal)
- Tricomegalia
- Tricomicosis axilar
- Tricorrexis invaginata (pelo de bambú)
- Tricorrexis nodosa
- Tricostasis espinulosa
- foliculitis en mechones
- Alopecia tumoral
- Distrofia de veinte uñas (uñas ásperas como papel de lija, traquioniquia)
- Síndrome del cabello inpeinable ( cheveux incoiffable , pili trianguli et canaliculi, cabello de vidrio hilado)
- Nevo de pelo lanoso (nevo de pelo lanoso)
- Hipertricosis ligada al cromosoma X
Condiciones de la grasa subcutánea
Las afecciones de la grasa subcutánea son aquellas que afectan la capa de tejido adiposo que se encuentra entre la dermis y la fascia subyacente . [ 36 ] [ 37 ] [ 38 ] [ 39 ]
- Lipodistrofia generalizada adquirida (síndrome de Lawrence, síndrome de Lawrence-Seip)
- Adiposis dolorosa (enfermedad de Dercum)
- Paniculitis por deficiencia de alfa-1 antitripsina (paniculitis por deficiencia de alfa1-proteasa, paniculitis por deficiencia de alfa1-proteinasa)
- paniculitis atrófica del tejido conectivo
- Síndrome de Barraquer-Simons (lipodistrofia parcial adquirida, lipodistrofia cefalotorácica, lipodistrofia progresiva)
- Lipomatosis simétrica benigna (lipomatosis simétrica benigna de Launois-Bensaude, enfermedad de Madelung)
- Lipodistrofia abdominal centrífuga (lipodistrofia centrífuga, lipodystrophia centrifugalis abdominalis infantalis)
- Eritema nodoso crónico (eritema nodoso migratorio, paniculitis migratoria subaguda de Vilanova y Piñol, paniculitis nodular migratoria subaguda)
eritema nodoso crónico - Paniculitis por frío (paniculitis por paletas heladas)
- Lipodistrofia generalizada congénita (síndrome de Berardinelli-Seip)
- paniculitis histiocítica citofágica
- Lipodistrofia inducida por fármacos
- Paniculitis facticia
- Lipodistrofia parcial familiar (síndrome de Köbberling-Dunnigan)
- paniculitis gotosa
- Síndrome de hemihiperplasia-lipomatosis múltiple
- Lipodistrofia asociada al VIH [ nb 8 ]
- lipoatrofia involutiva
- Lipoatrofia annularis (lipoatrofia de Ferreira-Marques)
- Lipoatrophia semicircularis (lipoatrofia semicircular)
- Lipodermatoesclerosis (paniculitis crónica con cambios lipomembranosos, hipodermitis esclerodermiforme, paniculitis esclerosante, paniculitis por estasis)
- Lipohipertrofia
- lipodistrofia localizada
- Paniculitis lobulillar neutrofílica
- vasculitis nodular
- Lipoatrofia hemifacial lineal de aparición tardía no progresiva
- Paniculitis pancreática (paniculitis enzimática, necrosis grasa pancreática, necrosis grasa subcutánea)
- Síndrome de Polonia
- Paniculitis post-esteroides
- Esclerema neonatal
- Lipogranuloma esclerosante (parafinoma)
- paniculitis septal
- Necrosis de la grasa subcutánea del recién nacido
- Paniculitis traumática
- Síndrome de lisis tumoral
- Enfermedad de Weber-Christian (paniculitis febril no supurativa recurrente)
Anomalías congénitas
Las anomalías congénitas cutáneas son un grupo diverso de trastornos que resultan de una morfogénesis defectuosa , el proceso biológico que da forma al cuerpo humano . [ 35 ] [ 40 ] [ 41 ]
- Uña accesoria del quinto dedo del pie
- Trago accesorio (etiqueta auricular, apéndice preauricular, etiqueta preauricular)
- Síndrome de bridas amnióticas (complejo ADAM, secuencia de bridas amnióticas, bridas congestivas, pseudoainhum)
- Aplasia cutis congénita (aplasia cutis, ausencia congénita de piel, cicatrices congénitas)
- Fístula arteriovenosa
- Hemangiomatosis neonatal benigna
- Quiste branquial (quiste de hendidura branquial)
- quiste broncogénico
- Hemangioma capilar (hemangioma infantil, nevus maternus, hemangioma en fresa, nevus en fresa)
- malformación venosa cavernosa
- Resto cartilaginoso congénito del cuello (trago cervical accesorio, papada)
- Dermatosis erosiva y vesicular congénita
- Hipertrofia congénita del pliegue lateral del dedo gordo del pie
- Fosa labial congénita (seno congénito del labio inferior, seno labial, seno de la línea media del labio superior)
- Malformaciones congénitas de los dermatoglifos
- Hamartoma congénito de músculo liso
- Malformación linfática quística
- quiste dermoide
- Hemangiomatosis neonatal difusa
- Encefalocele
- Comedones diseminados familiares sin disqueratosis [ 42 ]
- Displasia dérmica facial focal
- Los dientes de Hutchinson
- Malformación capilar-venosa cutánea hiperqueratósica
- Necrosis epidérmica intrauterina
- Síndrome mamario-extremidad
- Síndrome de Lowry-MacLean
- Macroqueilia
- Malformación linfática macroquística
- Pilomatricoma maligno (carcinoma pilomatricial, carcinoma pilomatricial)
- Enfermedad ampollosa autoinmune materna
- Quiste del rafe medio
- Tumor neuroectodérmico melanótico de la infancia
- Aplasia cutánea membranosa
- Malformación linfática microquística
- hendidura cervical de la línea media
- Mancha mongólica (melanocitosis dérmica congénita, melanocitosis dérmica)

lugar mongol - Molar de mora
- disostosis acrofacial de Nager
- Glioma nasal (heterotopia similar al cerebro, heterotopia cefálica similar al cerebro, hamartoma glial, tejido neuroglial heterotópico, heterotopia cerebral nasal, tejido cerebral heterotópico nasal)
- Quiste del conducto nasolagrimal
- Nevo psilolíparo
- Hemangioma congénito no involutivo
- Quiste del conducto onfalomesentérico (remanente del conducto onfalomesentérico, quiste vitelino)
- Síndrome de pelvis
- Pilomatricoma (epitelioma calcificante de Malherbe, epitelioma calcificante de Malherbe, pilomatrixoma)
- Anomalía de Polonia
- Malformaciones de la fosa posterior, hemangiomas, anomalías arteriales, defectos cardíacos, anomalías oculares, hendidura esternal y síndrome del rafe supraumbilical (asociación PHACE, síndrome PHACES)
- Seno y quiste preauricular (fosa auricular, fístula auricular congénita, fístula preauricular congénita, quiste preauricular)
- Hemangioma congénito de rápida involución (hemangioma congénito no progresivo)
- Síndrome de Rosenthal-Kloepfer
- Dedo supernumerario rudimentario (polidactilia rudimentaria)
- Síndrome sacro
- Seno pericraneal
- Hoyuelo en la piel (fosa cutánea)
- Malformación linfática superficial (linfangioma circunscrito)
- Pezón supernumerario (pezón accesorio, pseudomamá)
- quiste del conducto tirogloso
- Malformación vascular verrugosa (angiokeratoma circunscrito naeviforme)
Enfermedades del tejido conectivo
Las enfermedades del tejido conectivo son causadas por una compleja serie de respuestas autoinmunes que atacan o afectan al colágeno o a la sustancia fundamental . [ 35 ] [ 43 ]
- Lupus eritematoso cutáneo agudo
- Atrofodermia de Pasini y Pierini (variación discrómica y atrófica de la esclerodermia, morphea plana atrophica, sclérodermie atrophique d'emblée )
- Síndrome de calcinosis-fenómeno de Raynaud-dismotilidad esofágica-esclerodactilia-telangiectasias (síndrome CREST)
- Lupus eritematoso pernio (lupus eritematoso pernio de Hutchinson)
- Dermatomiositis infantil
- lupus eritematoso discoide infantil
- Lupus eritematoso sistémico infantil
- síndromes de deficiencia del complemento
- Dermatomiositis
- síndrome de Ehlers-Danlos
- Síndrome de eosinofilia-mialgia
- Esclerodermia lineal frontal ( en golpe de sable , morfea en golpe de sable )
esclerodermia lineal frontal - lupus eritematoso discoide generalizado
- morfea generalizada
- Dermatitis granulomatosa intersticial
- Artritis reumatoide juvenil (artritis idiopática juvenil, enfermedad de Still)
- Morfea queloide
- Atrofodermia lineal de Moulin (Moulin atrophoderma linearis)
- esclerodermia lineal
- lupus eritematoso discoide localizado
- morfea localizada
morfea localizada - Paniculitis por lupus eritematoso (lupus eritematoso profundo, paniculitis por lupus, lupus profundo, lupus eritematoso subcutáneo)
- Síndrome de superposición de lupus eritematoso y liquen plano (síndrome de superposición de liquen plano y lupus eritematoso)
- Erupción papular inducida por metotrexato
- Enfermedad mixta del tejido conectivo (síndrome de Sharp, enfermedad indiferenciada del tejido conectivo)
- Morphea profunda
- Superposición entre Morphea y liquen escleroso y atrófico
- Síndrome de úlceras bucales y genitales con inflamación del cartílago (síndrome MAGIC)
- lupus eritematoso neonatal
- Fibrosis sistémica nefrogénica (dermopatía fibrosante nefrogénica)
- Síndrome de Nicolau-Balus
- Síndrome de nodulosis-artropatía-osteólisis
- calcinosis tumoral familiar normofosfatémica
- Dermatitis neutrofílica y granulomatosa en empalizada
- Morfea pansclerótica
- Síndrome de Parry-Romberg (atrofia hemifacial progresiva)
- esclerosis sistémica progresiva
- Policondritis recidivante (policondritis atrófica, condromalacia sistémica)
- Artritis reumatoide
- Nodulosis reumatoide (nodulosis reumatoide acelerada)
- vasculitis reumatoide
- Síndrome de Rowell
- Scleredema adultorum (enfermedad de Bushke, escleredema diabeticorum, escleredema adultorum de Buschke, escleredema de Buschke)
- Silicosis
- Síndrome de Sjögren (enfermedad de Mikulicz, síndrome de Sicca)
- lupus eritematoso cutáneo subagudo
- lupus eritematoso sistémico
- Síndrome del petróleo tóxico
- Lupus eritematoso tumido (lupus eritematoso tumidus)
- Síndrome de Tuzun
- Lupus eritematoso verrugoso (lupus eritematoso hipertrófico)
- síndrome de Winchester
Anomalías del tejido fibroso y elástico dérmico

Las anomalías del tejido fibroso y elástico dérmico son causadas por problemas en la regulación de la síntesis o degradación del colágeno . [ 35 ] [ 44 ]
- Acrodermatitis crónica atrófica (enfermedad de Herxheimer, atrofia difusa primaria)
- Elastosis actínica (elastosis solar)
- Anetoderma (anetoderma maculosa, anetoderma maculosa cutis, atrofia maculosa cutis, atrofia macular)
- Blefarocalasia
- Cutis laxa (chalazodermia, dermatocalasia, dermatolisis, dermatomegalia, elastólisis generalizada, elastorrexis generalizada, paquidermatocele)
- Nuca romboidal de cutis
- Síndrome de Ehlers-Danlos (cutis hiperelástica, piel elástica, piel de caucho)
- Elastosis perforante serpiginosa
- homocistinuria
- Anetodermia de Jadassohn-Pellizzari
- Elastosis focal lineal (estrías elastóticas)
- Síndrome de Loeys-Dietz
- síndrome de Marfan
- Síndrome del cuerno occipital
- Osteogénesis imperfecta (síndrome de Lobstein)
- Elastosis calcificante perforante (pseudoxantoma elástico cutáneo adquirido localizado, elastosis calcificante periumbilical perforante, pseudoxantoma elástico perforante periumbilical)
- Pseudoxantoma elástico (síndrome de Grönblad-Strandberg)
- colagenosis perforante reactiva
- Anetodermia de Schweninger-Buzzi
- Fibroma esclerótico
- Estrías atróficas
- Estrías distensas
- enfermedad de Ullrich
- Colagenoma perforante verrugoso
- Síndrome de piel arrugada
Tumores dérmicos y subcutáneos
Los crecimientos dérmicos y subcutáneos resultan de (1) proliferación reactiva o neoplásica de componentes celulares de la dermis o del tejido subcutáneo , o (2) neoplasias que invaden o se presentan de forma aberrante en la dermis. [ 1 ] [ 35 ]
- Linfangioma progresivo adquirido (linfangioendotelioma benigno)
- Fibroqueratoma acral (fibroqueratoma digital adquirido, fibroqueratoma periungueal adquirido)
- Acrocordón (papiloma cutáneo, apéndice cutáneo, pólipo fibroepitelial, molusco contagioso, fibroma péndulo, papiloma cervical, apéndice cutáneo, fibroma blando, apéndice cutáneo de Templeton)
- Adenoma sebáceo
- Erupción generalizada de mastocitosis cutánea de tipo adulto
- sarcoma cutáneo de Kaposi africano
- Sarcoma de Kaposi linfadenopatía africana
- Fibromatosis infantil agresiva
- Sarcoma de Kaposi asociado al SIDA
- Ainhum ( bankokerend , dactilólisis espontánea, sukhapakla )
- Angiofibroma
- Angiokeratoma
- Angioqueratoma de Fordyce (angioqueratoma del escroto y la vulva)

Angiokeratoma de Fordyce - Angioqueratoma de Mibelli (angioqueratoma de Mibelli, verrugas telangiectásicas)
- Angioleiomioma (leiomioma vascular)
- Angiolipoleiomioma
- Angiolipoma
- Angioma serpiginoso
- Angiosarcoma
- Fibroma aponeurótico (fibroma aponeurótico calcificante, fibroma aponeurótico juvenil)
- fibroxantoma atípico
- Lipoblastomatosis benigna (lipoma embrionario)
- Síndrome de Buschke-Ollendorff (dermatofibrosis lenticular diseminada)
- Aneurismas capilares
- Carcinoide
- angiofibroma celular
- Angioma cereza (mancha de De Morgan, angioma senil)
- Condrodermatitis nodularis crónica helicis (condrodermatitis nodularis helicis)

Condrodermatitis nodular crónica helicis - lipoma condroide
- Cordoma
- Sarcoma de Kaposi clásico
- Fibroma colagenoso (fibroblastoma desmoplásico)
- hemangioendotelioma compuesto
- Nevo de tejido conectivo (colagenoma, elastoma, placa de shagreen)
- endometriosis cutánea
- Meningioma cutáneo (tejido meníngeo heterotópico, meningocele rudimentario)
- mielofibrosis cutánea
- Mixoma cutáneo
- Cutis marmorata telangiectatica congénita (flebectasia generalizada congénita, síndrome de Van Lohuizen)
- Hamartoma de dendrocitos dérmicos
- Dermatofibroma (histiocitoma fibroso benigno, dendrocitoma dérmico, dermatofibroma fibroso, histiocitoma fibroso, fibroma simple, histiocitoma, fibrosis subepidérmica nodular, hemangioma esclerosante)
- Dermatofibrosarcoma protuberans
- tumor desmoide
- mastocitosis cutánea difusa
- Fibromatosis infantil difusa
- Contractura de Dupuytren (diátesis de Dupuytren, enfermedad de Dupuytren, fibromatosis palmar)
- Hamartoma angiomatoso ecrino
- Elastofibroma dorsal
- Angioendotelioma papilar endovascular (tumor de Dabska, hemangioendotelioma tipo Dabska, hemangioendotelioma en forma de clavo, angioendotelioma papilar endovascular maligno, angioendotelioma intralinfático papilar)
- histiocitoma de células epitelioides
- hemangioendotelioma epitelioide
- sarcoma epitelioide
- mastocitosis eritrodérmica
- Condroma extraesquelético (condroma de partes blandas)
- Fibromas mixovasculares familiares
- Hernia fascial
- Fibroma de la vaina tendinosa
- Fibromatosis cervical (tumor esternocleidomastoideo infantil)
- Hamartoma fibroso de la infancia
- Pápula fibrosa de la nariz (pápula fibrosa solitaria benigna, pápula fibrosa de la cara)
- Pliegues en la piel con cicatrices (síndrome del bebé neumático Michelin)
- Mancha de Fordyce (enfermedad de Fordyce)

El lugar de Fordyce - quiste ganglionar
- Ganglioneuroma
- fibroma de Gardner
- Leiomioma genital (leiomioma dartoico)
- fibroblastoma de células gigantes
- Tumor de células gigantes de la vaina tendinosa (sinovioma de células gigantes, tenosinovitis nodular localizada, sinovitis villonodular pigmentada)
- hemangioma glomeruloide
- Tumor glómico (glomangioma, tumor glómico sólido, tumor glómico solitario)
- Tumor de células granulares (tumor de Abrikossoff, tumor de Abrikossov, mioblastoma de células granulares, tumor de la vaina nerviosa de células granulares, schwannoma de células granulares)
- Hamartoma
- Hemangiopericitoma
- Hemangiosarcoma
- Hibernoma (lipoma fetal, lipoma de grasa embrionaria, lipoma de tejido adiposo inmaduro)
- cicatriz hipertrófica
- Sarcoma de Kaposi asociado a inmunosupresión
- Fibromatosis digital infantil (fibromatosis por cuerpos de inclusión, miofibroblastoma digital infantil, tumor de Reye)
- Hemangiopericitoma infantil (hemangiopericitoma congénito)
- Miofibromatosis infantil (fibromatosis generalizada congénita, fibromatosis multicéntrica congénita)
- Hialinosis sistémica infantil (hialinosis sistémica juvenil)
- Lipoma intradérmico de células fusiformes
- Hiperplasia endotelial papilar intravascular ( hemangioendotelioma vegetante intravascular de Masson , lesión de Masson, pseudoangiosarcoma de Masson, tumor de Masson, hiperplasia endotelial papilar)
- Fibromatosis hialina juvenil (fibromatosis hyalinica multiplex juvenilis, síndrome de Murray-Puretic-Drescher)
- Hemangioendotelioma kaposiforme (hemangioendotelioma kaposiforme infantil)
- Síndrome de Kasabach-Merritt (hemangioma con trombocitopenia)
- Queloide (cicatriz queloide)

Queloide - metaplasia queratinizante
- Quiste queratoquístico
- Síndrome de Klippel-Trenaunay (síndrome de angioosteohipertrofia, hipertrofia hemangiectásica)
- almohadillas de los nudillos (heloderma)
- Leiomiosarcoma
- Lipoma
- Liposarcoma (lipoma atípico, tumor lipomatoso atípico)
- Linfangiectasia (linfangioma)
- Linfangiomatosis
- Histiocitoma fibroso maligno
- Tumor maligno de la vaina nerviosa periférica (schwannoma maligno, neurofibrosarcoma, neurosarcoma)
- sarcoma de mastocitos
- Meningocele
- Carcinoma metastásico
- Hemangioma microvenular (hemangioma microcapilar)
- Nevus flamígero de la línea media (beso de ángel, mancha salmón)
- Linfangioendoteliomatosis multifocal (angiomatosis cutaneovisceral congénita con trombocitopenia, linfangioendoteliomatosis multifocal con trombocitopenia)
- Angiohistocitoma de células multinucleadas
- Síndrome de leiomiomatosis cutánea y uterina múltiple (leiomiomatosis cutis et uteri, leiomiomatosis múltiple, síndrome de Reed)
- Leiomioma cutáneo múltiple (leiomioma pilar)
- Fibrolipoma neural
- Neuroblastoma (neuroblastoma infantil, neuroepitelioma)
- Neuroma cutis
- Neurotequeoma (neurofibroma cutáneo atípico, neuromixoma lobular cutáneo, mixoma de la vaina nerviosa, perineurioma mixomatoso, mixoma de la vaina nerviosa)
- Nevus flammeus (malformación capilar, mancha de vino de Oporto)
- Nevus flammeus nuchae (picadura de cigüeña)
- Nevo lipomatoso superficial (nevo lipomatoso de Hoffman y Zurhelle)
- Nevo oligémico
- Fascitis nodular (fascitis pseudosarcomatosa nodular, fascitis pseudosarcomatosa, fibromatosis pseudosarcomatosa subcutánea)
- Fibrosis submucosa oral
- Paquidermodactilia
- Neuroma encapsulado en empalizada
- Síndrome paraneoplásico
- Pápulas perladas del pene (hirsuties coronae glandis, papilomas hirsutoides)
- Enfermedad de Peyronie (induratio penis plastica)
- Facomatosis pigmentovascular
- Piloleiomioma
- Fibromatosis plantar (enfermedad de Ledderhose)
- Fibroma pleomórfico
- Lipoma pleomórfico
- Tumor fibrohistiocítico plexiforme
- Nevo porokeratósico de conductos ecrinos y dérmicos
- Histiocitoma nodular progresivo
- angioendoteliomatosis proliferativa
- Arteria labial inferior prominente
- Pseudo-ainhum
- Hemangioendotelioma retiforme (hemangioendotelioma en forma de clavo)
- Schwannoma (neuroma acústico, neurilemoma, neurinoma, neurolemoma, tumor de células de Schwann)
- Angiokeratoma solitario
- Leiomioma cutáneo solitario
- Mastocitoma solitario
- Neurofibroma solitario (neurofibroma plexiforme, tumor solitario de la vaina nerviosa, neurofibroma esporádico)
- Angioma aracniforme (nevus araneus, telangiectasia aracniforme, nevus aracniforme, araña vascular)
- Hemangioendotelioma de células fusiformes (hemangioma de células fusiformes)
- lipoma de células fusiformes
- hendidura esternal
- exostosis subungueal
- Fibromixoma acral superficial
- mastocitosis sistémica
- Hemangioma hemosiderótico en diana (hemangioma en forma de clavo)
- Telangiectasia
- Telangiectasia macular eruptiva persistente
- Teratoma
- Angioma en penacho (angioma en penacho adquirido, angioblastoma, angioblastoma de Nakagawa, hemangioma hipertrófico, hemangioma capilar progresivo, hemangioma en penacho)
- Granuloma umbilical
- Angiomatosis universal (telangiectasia generalizada)
- Urticaria pigmentosa (erupción generalizada de mastocitosis cutánea de tipo infantil)
- Lago venoso (flebectasia)
- Síndrome de Wildervanck
- mastocitosis xantelasmoidal
- metástasis zosteriforme
Dermatitis
La dermatitis es un término general para " inflamación de la piel". [ 45 ]
Atópico
La dermatitis atópica es una dermatitis crónica asociada a una predisposición hereditaria a desarrollar alergias a alimentos y sustancias inhaladas. [ 46 ] [ 47 ] [ 48 ]
- Dermatitis atópica (eccema atópico, neurodermatitis diseminada, eccema flexural, eccema infantil, prurigo diathsique)
Contacto
La dermatitis de contacto es causada por ciertas sustancias que entran en contacto con la piel. [ 49 ] [ 50 ] [ 51 ]
- Dermatitis por ácido abiético
- Inducido por ácido
- dermatitis por monómero acrílico
- Dermatitis adhesiva
- dermatitis africana por ébano
- Dermatitis por airbag (quemadura por airbag)
- Inducido por álcalis
- Alérgico
- Agente antifúngico inducido
- Agente antimicrobiano inducido
- dermatitis por arsénico
- Inducido por uñas artificiales
- Inducido por antitranspirante axilar
- Inducido por desodorante axilar
- Síndrome del babuino
- Dermatografismo negro
- crema blanqueadora inducida
- Inducido por capsaicina
- Quemadura química

Quemadura química - Cloracné
- dermatitis cromógena
- Inducido por la ropa
- Dermatitis por cobalto
- Estomatitis de contacto (reacción liquenoide de contacto, reacción liquenoide por amalgama, reacción de canela de la mucosa oral)
- Urticaria de contacto
- Inducido por corticosteroides
- dermatitis cosmética
- Síndrome de intolerancia cosmética
- Inducido por dentífrico
- Dermatitis causada por metales y sales metálicas
- Inducido por el polvo
- dermatitis por resina epoxi
- Inducido por etilendiamina
- maquillaje de ojos inducido
- dermatitis por fibra de vidrio
- Inducido por flores
- Inducido por formaldehído
- Agente liberador de formaldehído inducido
- Inducido por fragancia
- dermatitis dorada
- Decoloración del cabello inducida
- Inducido por tinte para el cabello
- inducido por loción capilar
- Inducido por laca para el cabello
- Inducido por alisador de cabello
- Tónico capilar inducido
- Inducido por plantas de interior
- Inducido por hidrocarburos
- foliculitis irritativa
- Dermatitis por laca (sensibilidad a la laca)
- Inducido por lanolina
- Inducido por lápiz labial
- Inducido por anestésico local
- dermatitis de ébano de Makassar
- Inducido por plantas marinas
- dermatitis irritativa mecánica
- dermatitis por mercurio
- Inducido por enjuague bucal
- Inducido por el esmalte de uñas
- inducido por quitaesmalte
- dermatitis por níquel
- Inducido por la ocupación
- Inducido por p-cloro-met-xilenol
- Inducido por parabenos
- dermatitis por parafenilendiamina
- Preparación de la permanente inducida
- Inducido por fármacos fenotiazínicos
- Fotoalérgico
- Fotoirritante
- Inducido por derivados de plantas
- Inducido por el polen
- dermatitis por resina de poliéster
- inducido por propilenglicol

dermatitis por Toxicodendro - dermatitis de contacto proteica
- Hipersensibilidad al Quaternium-15
- dermatitis de Reed
- dermatitis por palo de rosa
- dermatitis por resina
- dermatitis por goma
- Inducido por semillas
- dermatitis por calzado
- Inducido por solvente
- Inducido por ácido sórbico
- Dermatitis de contacto irritativa subjetiva (dermatitis de contacto irritativa sensorial)
- Inducido por protector solar
- Dermatitis de contacto sistémica
- Dermatitis por gas lacrimógeno
- dermatitis textil
- Dermatitis de contacto irritativa traumática
- Planta asociada a árboles inducida
- Inducido por el árbol
- dedos de tulipán
- Inducido por urushiol
- Inducido por vegetales
Eczema
El eccema se refiere a una amplia gama de afecciones que comienzan como dermatitis espongiótica y pueden progresar a una etapa liquenificada . [ 26 ] [ 52 ]

- dermatitis autoinmune por estrógenos
- Dermatitis autoinmune por progesterona
- dermatitis por autosensibilización
- Eczema mamario (eczema del pezón)
- eccema vesiculobulloso crónico de las manos
- eccema de la circunstomía
- Dishidrosis (eccema vesiculoampolloso agudo de las manos, cheiropompholyx, eczema Dishidrótico, pompholyx, podopompholyx)
- eccema de oído
- dermatitis palpebral
- eccema en las manos
- dermatitis hiperqueratósica de las manos
- Reacción idiopática (eczema diseminado, eccema generalizado)
- Dermatitis irritativa del pañal (dermatitis del pañal, dermatitis del pañal)
- Dermatosis plantar juvenil (pies atópicos de invierno, dermatitis plantaris secca, dermatitis del antepié, síndrome del pie de bota lunar, dermatitis por calcetines sudorosos)
- dermatitis por molusco
- Dermatitis numular (eccema discoide, eccema microbiano, eccema numular, neurodermatitis numular)
- eccema por deficiencia nutricional
- Síndrome de Sulzberger-Garbe (enfermedad oid-oid)
- Eczema xerótico (eczema asteatósico, dermatitis por desecación, eczema craquelado , prurito hiemal, eczema invernal, picazón invernal)
Pustuloso
La dermatitis pustulosa es una inflamación de la piel que se presenta con lesiones pustulosas . [ 26 ] [ 53 ]
- Foliculitis pustulosa eosinofílica (enfermedad de Ofuji, pustulosis eosinofílica estéril)
- Artritis reactiva
- Dermatosis pustulosa subcórnea (enfermedad de Sneddon-Wilkinson)
Seborreico
La dermatitis seborreica es una enfermedad inflamatoria crónica y superficial caracterizada por descamación sobre una base eritematosa . [ 54 ]
- Dermatitis seborreica infantil
- Enfermedad de Leiner
- Pitiriasis simplex capillitii (caspa)
- Dermatitis seborreica (eccema seborreico)
Alteraciones de la pigmentación
Las alteraciones de la pigmentación humana, ya sea pérdida o reducción, pueden estar relacionadas con la pérdida de melanocitos o la incapacidad de los melanocitos para producir melanina o transportar melanosomas correctamente. [ 55 ] [ 56 ] [ 57 ]
- Síndrome de albinismo-mechón negro-trastorno de la migración celular de los neurocitos del intestino-sordera (síndrome ABCD)
- Síndrome de albinismo y sordera (síndrome de Woolf, síndrome de Ziprkowski-Margolis)
- Síndrome de Alezzandrini
- Argiria
- Envenenamiento por arsénico
Vitíligo - síndrome de Berlín
- Cambios en la pigmentación causados por la bioacumulación de pigmentos, por ejemplo, cantaxantina.
- Síndrome de Chédiak-Higashi
- Crisiasis
- Síndrome de Cross-McKusick-Breen (síndrome de Cross, síndrome de hipopigmentación oculocerebral)
- Dermatopatía pigmentosa reticularis (dermatopatía pigmentosa reticularis hiperqueratósica y mutilante, dermatopatía pigmentosa reticularis hipohidrótica y atrófica, dermatopatía pigmentosa reticularis)
- Discromatosis simétrica hereditaria (acropigmentación reticulada de Dohi, discromatosis simétrica de las extremidades)
- Discromatosis universal hereditaria
- Síndrome de Elejalde (síndrome de Griscelli tipo 1)
- hipomelanosis eruptiva
- Hiperpigmentación progresiva familiar
- Enfermedad de Galli-Galli
- Síndrome de Griscelli tipo 2 (albinismo parcial con inmunodeficiencia)
- Síndrome de Griscelli tipo 3
- Hemocromatosis (diabetes bronceada)
- Hiperpigmentación por hemosiderina
- Síndrome de Hermansky-Pudlak
- Hipomelanosis guttata idiopática (leucopatía simétrica progresiva)
- decoloración metálica del hierro
- Síndrome de Klein-Waardenburg
- Saturnismo
- Leucodermia
- Leucodermia asociada al melanoma
- Melasma (cloasma faciei, máscara del embarazo)
- Síndrome de Mukamel
- Collar de Venus
- Nevo anémico

Nevo anémico - Nevo despigmentoso (nevo acrómico)
- albinismo ocular
- albinismo oculocutáneo
- Síndrome de Pallister-Killian
- Hiperpigmentación periorbitaria
- Fotoleucomelanodermatitis de Kobori
- hipomelanosis filoide
- Piebaldismo
- Pigmentación reticular facial y coli
- Pitiriasis alba
- Poiquilodermia de Civatte
- Poiquiloderma vascular atrófico
- Hiperpigmentación postinflamatoria (hipermelanosis postinflamatoria)
- hipopigmentación postinflamatoria
- Hipomelanosis macular progresiva
- vitíligo cuadricrómico
- Anomalía pigmentada reticular de los pliegues (enfermedad de los puntos oscuros, enfermedad de Dowling-Degos)
- Acropigmentación reticulada de Kitamura
- Síndrome de Revesz
- melanosis de Riehl
- Dermatitis por rascado (pigmentación flagelada por bleomicina)
- Vitiligo segmentario
- Síndrome de Shah-Waardenburg
- Dermatitis por setas shiitake (dermatitis por setas flageladas, enfermedad del trabajador de setas, toxicodermia inducida por shiitake)
- melanosis por alquitrán (melanodermatitis tóxica liquenoide)
- síndrome de Tietz
- decoloración metálica del titanio
- Melanosis pustulosa neonatal transitoria (pustulosis neonatal transitoria, lentigos neonatorum)
- Vitíligo tricrómico
- Leucomelanoderma del vagabundo
- mácula vasoespástica
- Vitíligo
- Vitiligo ponctué
- Síndrome de Vogt-Koyanagi-Harada
- síndrome de Waardenburg
- Síndrome de Wende-Bauckus (síndrome de Pegum)
- El anillo de Woronoff
- Trastorno pigmentario reticular ligado al cromosoma X (amiloidosis cutánea familiar, amiloidosis de Partington, amiloidosis cutánea de Partington, síndrome de Partington tipo II, trastorno pigmentario reticular, trastorno pigmentario reticular ligado al cromosoma X con manifestaciones sistémicas)
- Síndrome de hipopigmentación sordociego yemení
erupciones cutáneas inducidas por fármacos
Las erupciones cutáneas son reacciones adversas a medicamentos que se presentan con manifestaciones cutáneas. [ 58 ] [ 59 ] [ 60 ]
- Acrodinia (enfermedad del calomelano, polineuropatía eritredémica, enfermedad rosada)
- Pustulosis exantemática generalizada aguda (erupción pustulosa inducida por fármacos, pustulodermia tóxica)

Pustulosis exantemática generalizada aguda - Reacción adversa a agentes biológicos
- Reacción adversa a las citoquinas
- Síndrome de hipersensibilidad al alopurinol
- Necrosis cutánea inducida por anticoagulantes
- Síndrome de hipersensibilidad a los anticonvulsivos
- Bromoderma
- Reacción farmacológica ampollosa (erupción farmacológica ampollosa, erupción fija generalizada por fármacos, erupción fija multilocular por fármacos)
- Eritema acral inducido por quimioterapia (síndrome de eritrodisestesia palmoplantar)
- Hiperpigmentación inducida por quimioterapia
- acné inducido por fármacos
- Angioedema inducido por fármacos
- Hiperplasia gingival relacionada con fármacos
- Reacción liquenoide inducida por fármacos (liquen plano inducido por fármacos, erupción liquenoide por fármacos)
- Lupus eritematoso inducido por fármacos
- Cambios en las uñas inducidos por fármacos
- pigmentación inducida por fármacos
- Urticaria inducida por fármacos
- Reacción farmacológica con eosinofilia y síntomas sistémicos.
- Eritema multiforme mayor (eritema multiforme menor – eritema multiforme de Hebra)
- dermatitis hiponiquial exudativa
- Reacción fija al fármaco
- Halogenoderma
- necrosis por heparina
- reacción adversa a medicamentos relacionada con la enfermedad del VIH
- dermatopatía por hidroxiurea
- Reacción en el lugar de la inyección
- Yododerma
- Síndrome de Churg-Strauss asociado a antagonistas del receptor de leucotrienos
- Dermatosis ampollosa lineal por IgA (dermatosis lineal por IgA)
- reacción farmacológica fotosensible
- síndrome del hombre rojo
- Reacciones cutáneas adversas graves (incluye síndrome DRESS , síndrome de Stevens-Johnson , necrólisis epidérmica tóxica , síndrome de superposición de Stevens-Johnson/necrólisis epidérmica tóxica y pustulosis exantemática generalizada aguda ).
- Reacción similar a la esclerodermia a los taxanos
- Reacción similar a la enfermedad del suero
- acné por esteroides
- foliculitis esteroidea
- Síndrome de Stevens-Johnson
- Síndrome de hipersensibilidad a las sulfonamidas
- Enfermedad de Texier
- Necrólisis epidérmica tóxica (síndrome de Lyell)
- Eritema urticarial multiforme
- Reacción a la vitamina K
- necrosis por warfarina
Relacionado con el sistema endocrino
Las afecciones endocrinas a menudo presentan manifestaciones cutáneas, ya que la piel interactúa con el sistema endocrino de muchas maneras. [ 61 ] [ 62 ]
- Acantosis nigricans asociada a malignidad (acantosis nigricans tipo I)
- Acantosis nigricans asociada a obesidad, estados de resistencia a la insulina y endocrinopatía (acantosis nigricans tipo III)
- Acantosis nigricans acral (anomalía acantótica acral)
Gangrena seca acral - Gangrena seca acral
- Acromegalia
- Enfermedad de Addison
- Adenoma suprarrenal
- Carcinoma suprarrenal
- Hiperplasia suprarrenal
- Síndrome de alopecia, distrofia ungueal, complicaciones oftálmicas, disfunción tiroidea, hipohidrosis, efélides y enteropatía, infecciones del tracto respiratorio (OTRO síndrome)
- arrenoblastoma
- Cretinismo
- Síndrome de Cushing

Acantosis nigricans asociada a obesidad, estados de resistencia a la insulina y endocrinopatía. - Síndrome de liberación excesiva de andrógenos ováricos (síndrome SAHA ovárico)
- Acantosis nigricans familiar (acantosis nigricans tipo II)
- deficiencia de la hormona del crecimiento
- Síndrome de hiperandrogenismo, resistencia a la insulina y acantosis nigricans (síndrome HAIR-AN)
- Hiperparatiroidismo
- Síndrome SAHA hiperprolactinémico
- Hipertiroidismo
- Hipoparatiroidismo
- Hipotiroidismo
- tumor de células de Leydig
- Neoplasia endocrina múltiple tipo 1 (síndrome de Wermer)
- Neoplasia endocrina múltiple tipo 2 (neoplasia endocrina múltiple tipo 2A, feocromocitoma y carcinoma medular de tiroides productor de amiloide, síndrome PTC, síndrome de Sipple)
- Neoplasia endocrina múltiple tipo 3 (neuromas mucosos con tumores endocrinos, neoplasia endocrina múltiple tipo 2B, síndrome de neuroma mucoso múltiple, síndrome de Wagenmann-Froboese)
- mixedema
- Panhipopituitarismo
- Síndrome de adrenarquia persistente (síndrome SAHA suprarrenal)
- Síndrome de ovario poliquístico
- Seborrea-acné-hirsutismo-alopecia (síndrome SAHA)
- acropaquia tiroidea
Eosinófilo
Las afecciones cutáneas eosinofílicas abarcan una amplia variedad de enfermedades que se caracterizan histológicamente por la presencia de eosinófilos en el infiltrado inflamatorio o por evidencia de degranulación de eosinófilos . [ 63 ] [ 64 ]
- Hiperplasia angiolinfoide con eosinofilia (hemangioma epitelioide, hemangioma histiocitoide, nódulo angiomatoso inflamatorio, hemangioma arteriovenoso inflamatorio, proliferación vascular atípica intravenosa, angioplasia papular, granuloma pseudopiógeno)
- Eritema anular infantil
- ataque de artrópodos
- Celulitis eosinofílica (síndrome de Wells)
- Fascitis eosinofílica (síndrome de Shulman)
- Granuloma eosinofílico
- Granulomatosis eosinofílica con poliangitis
- Foliculitis pustulosa eosinofílica de la infancia (foliculitis pustulosa eosinofílica en la infancia, foliculitis pustulosa eosinofílica infantil, foliculitis pustulosa eosinofílica neonatal)
- Úlcera eosinofílica de la mucosa oral (úlcera eosinofílica de la lengua, enfermedad de Riga-Fede, granuloma eosinofílico traumático)
Úlcera eosinofílica de la mucosa oral - vasculitis eosinofílica
- Eritema tóxico neonatal (eritema tóxico, eritema tóxico del recién nacido)
- Granuloma facial
- Hipereosinofilia
- Síndrome hipereosinofílico
- Incontinencia pigmentaria (síndrome de Bloch-Siemens, enfermedad de Bloch-Sulzberger, síndrome de Bloch-Sulzberger)
- Enfermedad de protuberancias rojas con picazón (dermatitis papular)
- Xantogranuloma juvenil
- Enfermedad de Kimura
- Síndrome de nódulos, eosinofilia, reumatismo, dermatitis e hinchazón
- Dermatitis eosinofílica paquidérmica
- Erupción papular en personas negras
- Papuloeritrodermia de Ofuji
- Erupción papular pruriginosa de la enfermedad por VIH
Nevos epidérmicos, neoplasias y quistes
Los nevos epidérmicos , las neoplasias y los quistes son lesiones cutáneas que se desarrollan a partir de la capa epidérmica de la piel. [ 8 ] [ 26 ]
- Carcinoma basocelular aberrante
- Acantoma fisurado (granuloma fisurado, acantoma en montura de gafas)
- Acrospiroma (hidradenoma de células claras, tumor de conducto dérmico, hidroacantoma simple, hidradenoma nodular, poroma)
- Queratosis actínica (queratosis senil, queratosis solar)
- Carcinoma de células escamosas adenoideo (carcinoma de células escamosas pseudoglandular)
- Adenocarcinoma papilar digital agresivo (adenocarcinoma papilar digital, adenoma papilar)
Carcinoma basocelular - carcinoma de glándula apocrina
- nevo apocrino
- queratosis arsenical
- queratosis actínica atrófica
- Balanitis plasmacelular (balanopostitis crónica circumscripta plasmacelular, balanitis circumscripta plasmacelular, balanitis de células plasmáticas, vulvitis de células plasmáticas, vulvitis circunscripta plasmacelular, balanitis de Zoon, eritroplasia de Zoon, vulvitis de Zoon)
- Carcinoma basocelular
- hamartoma folicular basaloide
- Carcinoma de células escamosas basaloide
- Síndrome de Birt-Hogg-Dubé
- Enfermedad de Bowen (carcinoma de células escamosas in situ )
- Síndrome de Brooke-Fordyce
- Ceruminoma
- Carcinoma basocelular cicatricial (carcinoma basocelular morfeiforme, carcinoma basocelular morfeiforme)
- Quiste ciliado de la vulva (quiste mülleriano cutáneo, quiste mucinoso paramesonéfrico de la vulva)
- Acantoma de células claras (acanthome cellules claires of Degos and Civatte, acantoma de Degos, acantoma de células pálidas)
- Carcinoma de células escamosas de células claras (carcinoma de células claras de la piel)
- Queratosis cicatricial crónica (queratosis cicatrizal crónica)
- queratosis seborreica clonal
- queratosis seborreica común (papiloma de células basales, queratosis seborreica sólida)
- Síndrome de Cowden (enfermedad de Cowden, síndrome de hamartomas múltiples)
- Quiste cutáneo ciliado
- Quiste columnar cutáneo
- Cuerno cutáneo (Cornu cutaneum)
- Carcinoma basocelular quístico
- Cilindroma ecrino dérmico (cilindroma)
- Dermatosis papulosa negra
- tricoepitelioma desmoplásico
- Poro dilatado (poro dilatado de Winer)

enfermedad de Bowen - Carcinoma ecrino (carcinoma siringoide)
- nevo ecrino
- Quiste epidérmico (quiste de inclusión epidérmica, quiste epidermoide, quiste infundibular, quiste de queratina)
- Síndrome del nevus epidérmico (síndrome de Feuerstein y Mims, síndrome de Solomon)
- acantoma epidermolítico
- Epitelioma cuniculatum (tumor de Ackerman, carcinoma cuniculatum)
- quiste de vello eruptivo
- Eritroplasia de Queyrat
- Enfermedad de Paget extramamaria
- Fibroepitelioma
- Fibroepitelioma de Pinkus
- Fibrofoliculoma
- Quiste híbrido folicular (quiste híbrido)
- Hamartoma foliculosebáceo-apocrino (hamartoma folicular-apocrino)
- Hamartoma quístico foliculosebáceo
- Queratoacantoma eruptivo generalizado (queratoacantoma eruptivo generalizado de Grzybowski)
- Tricoepitelioma solitario gigante
- hidradenoma

hidradenoma - hidradenocarcinoma
- Hidrocistoma (cistadenoma, quiste de la glándula de Moll, quiste sudoríparo)
- Queratosis por hidrocarburos (queratosis por brea, queratosis por alquitrán, verruga por alquitrán)
- Hiperqueratosis lenticular persistente (enfermedad de Flegel)
- Hiperqueratosis del pezón y la areola
- queratosis actínica hiperqueratósica
- Ictiosis hystrix (ictiosis hystrix gravior tipo Lambert, hombre puercoespín, nevo verrugoso sistematizado)
- Ictiosis hystrix de Curth-Macklin
- carcinoma basocelular infiltrante
- Nevo epidérmico verrugoso lineal inflamatorio
- queratosis folicular invertida
- Queratosis seborreica irritada (acantoma basoescamoso, queratosis seborreica inflamada)
- Istmicoma (infundibuloma, tumor del infundíbulo folicular)
- Leucemia mielomonocítica juvenil
- quiste de implantación de queratina
- Queratoacantoma
- Queratoacantoma centrífugo marginado
- acantoma de células grandes
- queratosis actínica liquenoide
- queratosis liquenoide (queratosis liquenoide benigna, queratosis similar al liquen plano, liquen plano solitario, queratosis liquenoide solitaria)
- Nevo epidérmico verrugoso lineal (nevo epidérmico lineal, nevo epidérmico verrugoso)
- Acrospiroma maligno (espiradenocarcinoma)
- Tumor mixto maligno ( siringoma condroide maligno )
- Quiste tricolemal maligno
- Mantleoma
- Úlcera de Marjolin
- Melanoacantoma (queratosis seborreica pigmentada)
- Carcinoma de células de Merkel (apudoma cutáneo, carcinoma neuroendocrino primario de la piel, carcinoma primario de células pequeñas de la piel, carcinoma trabecular de la piel)
- Carcinoma anexial microquístico (carcinoma esclerosante de los conductos sudoríparos)
- carcinoma basocelular micronodular
- Milia en placa
- Milium

Milium - Tumor mixto ( siringoma condroide )
- Carcinoma mucinoso
- Nevo mucinoso (nevus mucinosus)
- Síndrome de Muir-Torre
- Tricoepitelioma familiar múltiple (síndrome de Brooke-Spiegler, epitelioma adenoide quístico)
- Queratoacantomas múltiples (síndrome de Ferguson-Smith, queratoacantomas múltiples de tipo Ferguson-Smith que se curan espontáneamente, queratoacantomas múltiples del tipo Ferguson-Smith)
- Hiperqueratosis digitiforme múltiple (queratosis digitiforme, hiperqueratosis espiculada diseminada, hiperqueratosis piliforme diseminada familiar, queratosis agregada diminuta)
- Síndrome de carcinoma basocelular nevoide (síndrome del nevo basocelular, síndrome de Gorlin, síndrome de Gorlin-Goltz)
- Nevus comedonicus (comedón nevo)
- Síndrome del nevus comedónico
- Nevo sebáceo (nevo sebáceo de Jadassohn, nevo organoide)
- Nevus unius lateris
- Carcinoma basocelular nodular (carcinoma basocelular clásico)
- Enfermedad de Paget de la mama
- Adenoma ecrino papilar (adenoma apocrino tubular)
- Hidradenoma papilar (hidradenoma papilífero)
- Papilomatosis cutánea carcinoide (papilomatosis carcinoide de Gottron, papilomatosis cutánea carcinoide de Gottron-Eisenlohr)
- Nevo azul en parche (melanocitosis dérmica adquirida, hamartoma de melanocitos dérmicos)
- fibroma perifolicular
- Facomatosis pigmentoqueratósica
- queratosis actínica pigmentada
- Carcinoma basocelular pigmentado
- Síndrome del nevus epidérmico piloso pigmentado
- acantoma de la vaina del pilar
- Seno pilonidal (seno pilonidal interdigital de Barber, quiste pilonidal, enfermedad pilonidal)
- Porocarcinoma (poroma maligno, porocarcinoma ecrino) [ 65 ] [ 66 ]
- carcinoma basocelular polipoide
- Carcinoma basocelular con aspecto de poro
- Carcinoma adenoide quístico cutáneo primario
- Quiste epidermoide proliferante (quiste epitelial proliferante)
- Quiste tricolemal proliferante (tumor pilar, neoplasia quística folicular proliferante, tumor pilar proliferante, tumor tricolemal proliferante)
- Pseudoquiste del pabellón auricular (pseudoquiste endocondrial auricular, condromalacia quística, pseudoquiste endocondral, quiste intracartilaginoso)
- Pseudoepitheliomatous keratotic and micaceous balanitis
- PUVA keratosis
- Rasmussen syndrome
- Reactional keratosis
- Reticulated seborrheic keratosis (adenoid seborrheic keratosis)
- Rodent ulcer (Jacobi ulcer)
- Schimmelpenning syndrome (Schimmelpenning–Feuerstein–Mims syndrome)
- Sebaceoma (sebaceous epithelioma)
- Sebaceous adenoma
- Sebaceous carcinoma
- Sebaceous hyperplasia
- Sebaceous nevus syndrome
- Seboacanthoma
- Seborrheic keratosis (seborrheic verruca, senile wart)
- Seborrheic keratosis with squamous atypia
- Signet-ring cell squamous cell carcinoma
- Solitary keratoacanthoma (subungual keratoacanthoma)
- Solitary trichoepithelioma
- Spindle cell squamous cell carcinoma (spindle cell carcinoma)
- Spiradenoma
- Squamous cell carcinoma

Squamous cell carcinoma - Steatocystoma multiplex (epidermal polycystic disease, sebocystomatosis)
- Steatocystoma simplex (simple sebaceous duct cyst, solitary steatocystoma)
- Stucco keratosis (digitate seborrheic keratosis, hyperkeratotic seborrheic keratosis, keratosis alba, serrated seborrheic keratosis, verrucous seborrheic keratosis)
- Superficial basal cell carcinoma (superficial multicentric basal cell carcinoma)
- Syringadenoma papilliferum (syringocystadenoma papilliferum)
- Syringofibroadenoma (acrosyringeal nevus of Weedon and Lewis)
- Syringoma
- Systematized epidermal nevus
- Thermal keratosis
- Trichilemmal carcinoma
- Trichilemmal cyst (isthmus-catagen cyst, pilar cyst)
- Trichilemmoma
- Trichoadenoma (trichoadenoma of Nikolowski)
- Trichoblastoma
- Trichoblastic fibroma
- Trichodiscoma
- Trichofolliculoma
- Unilateral palmoplantar verrucous nevus
- Urethral caruncle
- Verrucous carcinoma
- Verrucous cyst (cystic papilloma)
- Viral keratosis
- Warty dyskeratoma (isolated dyskeratosis follicularis)
- Waxy keratosis of childhood (kerinokeratosis papulosa)
- Zoon's vulvitis
- Zosteriform speckled lentiginous nevus
Erythemas

Erythemas are reactive skin conditions in which there is blanchable redness.[1][9]
- Erythema annulare centrifugum (deep gyrate erythema, erythema perstans, palpable migrating erythema, superficial gyrate erythema)
- Erythema gyratum repens (Gammel's disease)
- Erythema migrans (erythema chronicum migrans)
- Erythema multiforme
- Erythema multiforme minor (herpes simplex-associated erythema multiforme)
- Erythema palmare
- Generalized erythema
- Necrolytic acral erythema
- Necrolytic migratory erythema (glucagonoma syndrome)
Genodermatoses
Genodermatoses are inherited genetic skin conditions often grouped into three categories: chromosomal, single gene, and polygenetic.[67][68]
- 18q deletion syndrome
- Acrodermatitis enteropathica
- Acrogeria (Gottron syndrome)
- Acrokeratosis verruciformis (acrokeratosis verruciformis of Hopf)
- Adams–Oliver syndrome
- Adducted thumbs syndrome
- Albright's hereditary osteodystrophy
- Angelman syndrome
- Apert syndrome (acrocephalosyndactyly)
- Arthrogryposis–renal dysfunction–cholestasis syndrome
- Ataxia telangiectasia (Louis–Bar syndrome)
- Atrichia with papular lesions (papular atrichia)
- Atrophodermia vermiculata (acne vermoulante, acne vermoulanti, atrophoderma reticulata symmetrica faciei, atrophoderma reticulatum, atrophoderma vermiculata, atrophoderma vermiculatum, atrophodermia reticulata symmetrica faciei, atrophodermia ulerythematosa, atrophodermie vermiculée des joues avec kératoses folliculaires, folliculitis ulerythema reticulata, folliculitis ulerythematous reticulata, folliculitis ulerythemosa, honeycomb atrophy, ulerythema acneforme, ulerythema acneiforme)
- Autoimmune polyendocrinopathy–candidiasis–ectodermal dystrophy syndrome
- Bart syndrome
- Bazex–Dupré–Christol syndrome (Bazex syndrome, follicular atrophoderma and basal cell carcinomas)
- Beare–Stevenson cutis gyrata syndrome
- Bloom syndrome (Bloom–Torre–Machacek syndrome)
- Blue rubber bleb nevus syndrome
- Brittle hair–intellectual impairment–decreased fertility–short stature syndrome
- Cantú syndrome
- Cardio-facio-cutaneous syndrome (cardiofaciocutaneous syndrome)
- Cartilage–hair hypoplasia (McKusick type metaphyseal chondrodysplasia)
- Cerebral dysgenesis–neuropathy–ichthyosis–keratoderma syndrome
- Childhood tumor syndrome
- Chondrodysplasia punctata
- Cicatricial junctional epidermolysis bullosa
- Craniosynostosis–anal anomalies–porokeratosis syndrome
- Cockayne syndrome
- Colobomas of the eye–heart defects–ichthyosiform dermatosis–mental retardation–ear defects syndrome (CHIME syndrome, Zunich neuroectodermal syndrome, Zunich–Kaye syndrome)
- Congenital hemidysplasia with ichthyosiform erythroderma and limb defects syndrome (CHILD syndrome)
- Conradi–Hünermann syndrome (Conradi–Hünermann–Happle syndrome, Happle syndrome, X-linked dominant chondrodysplasia punctata)
- Costello syndrome
- Cronkhite–Canada syndrome
- Crouzon syndrome
- Cutis verticis gyrata
- Darier's disease (Darier–White disease, dyskeratosis follicularis, keratosis follicularis)

Linear Darier disease - DeSanctis–Cacchione syndrome
- Disseminated superficial actinic porokeratosis
- Disseminated superficial porokeratosis
- Dolichol kinase deficiency
- Dominant dystrophic epidermolysis bullosa
- Dyskeratosis congenita (Zinsser–Cole–Engman syndrome)
- Dystrophic epidermolysis bullosa
- Ectodermal dysplasia
- Ectodermal dysplasia with corkscrew hairs
- Ectrodactyly–ectodermal dysplasia–cleft syndrome (EEC syndrome, split hand–split foot–ectodermal dysplasia–cleft syndrome)
- Epidermolysis bullosa herpetiformis (Dowling–Meara epidermolysis bullosa simplex)
- Epidermolysis bullosa simplex
- Epidermolysis bullosa simplex of Ogna
- Epidermolysis bullosa simplex with mottled pigmentation
- Epidermolysis bullosa simplex with muscular dystrophy
- Epidermolytic hyperkeratosis (bullous congenital ichthyosiform erythroderma, bullous ichthyosiform erythroderma)
- Erythrokeratodermia with ataxia (Giroux–Barbeau syndrome)
- Familial benign chronic pemphigus (familial benign pemphigus, Hailey–Hailey disease)
- Fanconi syndrome (familial pancytopenia, familial panmyelophthisis)
- Fibrodysplasia ossificans progressiva
- Focal dermal hypoplasia (Goltz syndrome)
- Follicular atrophoderma
- Franceschetti–Klein syndrome (mandibulofacial dysostosis)
- Gardner's syndrome (familial colorectal polyposis)
- Gastrocutaneous syndrome
- Generalized atrophic benign epidermolysis bullosa
- Generalized epidermolysis bullosa simplex (Koebner variant of generalized epidermolysis bullosa simplex)
- Generalized trichoepithelioma
- Giant axonal neuropathy with curly hair
- Gingival fibromatosis with hypertrichosis
- Haber syndrome
- Hallerman–Streiff syndrome
- Harlequin-type ichthyosis (harlequin baby, harlequin fetus, harlequin ichthyosis, ichthyosis congenita, ichthyosis congenita gravior)
- Hay–Wells syndrome (AEC syndrome, ankyloblepharon filiforme adnatum–ectodermal dysplasia–cleft palate syndrome, ankyloblepharon–ectodermal defects–cleft lip and palate syndrome, ankyloblepharon–ectodermal dysplasia–clefting syndrome)
- Hereditary sclerosing poikiloderma

Keratosis pilaris - Heterochromia iridum
- Holocarboxylase synthetase deficiency
- Hypohidrotic ectodermal dysplasia (anhidrotic ectodermal dysplasia, Christ–Siemens–Touraine syndrome)
- Hypotrichosis–acro-osteolysis–onychogryphosis–palmoplantar keratoderma–periodontitis syndrome
- Hypotrichosis–lymphedema–telangiectasia syndrome
- Ichthyosis–brittle hair–impaired intelligence–decreased fertility–short stature syndrome (IBIDS syndrome, sulfur-deficient brittle hair syndrome, Tay's syndrome, trichothiodystrophy, trichothiodystrophy with ichthyosis)
- Ichthyosis bullosa of Siemens (ichthyosis exfoliativa)
- Ichthyosis follicularis (ichthyosis follicularis with alopecia and photophobia syndrome)
- Ichthyosis linearis circumflexa
- Ichthyosis prematurity syndrome
- Ichthyosis vulgaris (autosomal dominant ichthyosis, ichthyosis simplex)
- Ichthyosis with confetti
- Neonatal ichthyosis–sclerosing cholangitis syndrome (ichthyosis–sclerosing cholangitis syndrome, NISCH syndrome)
- Incontinentia pigmenti achromians (hypomelanosis of Ito)
- Immune dysfunction–polyendocrinopathy–enteropathy–X-linked syndrome
- Jaffe–Campanacci syndrome
- Johanson–Blizzard syndrome
- Johnson–McMillin syndrome
- Joubert syndrome
- Junctional epidermolysis bullosa
- Junctional epidermolysis bullosa gravis (epidermolysis bullosa letalis, Herlitz disease, Herlitz epidermolysis bullosa, Herlitz syndrome, lethal junctional epidermolysis bullosa)
- Junctional epidermolysis bullosa with pyloric atresia
- Kabuki syndrome (Kabuki makeup syndrome, Niikawa–Kuroki syndrome)
- Keratolytic winter erythema (erythrokeratolysis hiemalis, Oudtshoorn disease, Oudtshoorn skin)
- Keratosis follicularis spinulosa decalvans (Siemens-1 syndrome)
- Keratosis linearis with ichthyosis congenita and sclerosing keratoderma syndrome
- Keratosis pilaris atrophicans faciei (folliculitis rubra, keratosis pilaris rubra atrophicans faciei, lichen pilare, lichen pilaire ou xerodermie pilaire symmetrique de la face, ulerythema ophryogenes, xerodermi pilaire symmetrique de la face)
- Keratosis pilaris
- Kindler syndrome (acrokeratotic poikiloderma, bullous acrokeratotic poikiloderma of Kindler and Weary, congenital poikiloderma with blisters and keratoses, congenital poikiloderma with bullae and progressive cutaneous atrophy, hereditary acrokeratotic poikiloderma, hyperkeratosis–hyperpigmentation syndrome, Weary–Kindler syndrome)
- Klinefelter syndrome
- Klippel–Feil syndrome
- Lamellar ichthyosis (collodion baby)
- Legius syndrome (neurofibromatosis type 1-like syndrome)
- Lelis syndrome
- Lenz–Majewski syndrome
- Leschke syndrome
- Lethal acantholytic epidermolysis bullosa
- Lhermitte–Duclos disease
- Linear and whorled nevoid hypermelanosis (linear nevoid hyperpigmentation, progressive cribriform and zosteriform hyperpigmentation, reticulate and zosteriform hyperpigmentation, reticulate hyperpigmentation of Iijima and Naito and Uyeno, zebra-like hyperpigmentation in whorls and streaks, zebra-line hyperpigmentation)
- Linear Darier disease (acantholytic dyskeratotic epidermal nevus)
- Linear porokeratosis
- Localized epidermolysis bullosa simplex (Weber–Cockayne syndrome, Weber–Cockayne variant of generalized epidermolysis bullosa simplex)
- Mandibuloacral dysplasia
- Marinesco–Sjögren syndrome
- McCune–Albright syndrome
- McCusick syndrome
- Metageria
- Microphthalmia–dermal aplasia–sclerocornea syndrome
- Mitis junctional epidermolysis bullosa (nonlethal junctional epidermolysis bullosa)
- Mitochondrial myopathy–encephalopathy–lactic acidosis–stroke syndrome
- Multiple lentigines syndrome (cardiocutaneous syndrome, Gorlin syndrome II, lentiginosis profusa syndrome, LEOPARD syndrome, progressive cardiomyopathic lentiginosis)
- Multiple pterygium syndrome
- Multiple sulfatase deficiency (Austin disease, mucosulfatidosis)
- Naegeli–Franceschetti–Jadassohn syndrome (chromatophore nevus of Naegeli)
- Netherton syndrome
- Neurofibromatosis type 1 (von Recklinghausen's disease)

Neurofibromatosis type 1 - Neurofibromatosis type 3 (neurofibromatosis mixed type)
- Neurofibromatosis type 4 (neurofibromatosis variant type)
- Neutral lipid storage disease (Dorfman–Chanarin syndrome)
- Nonbullous congenital ichthyosiform erythroderma (congenital ichthyosiform erythroderma)
- Noonan syndrome
- Oculocerebrocutaneous syndrome (Delleman–Oorthuys syndrome)
- Oculodentodigital dysplasia
- Odonto-tricho-ungual-digital-palmar syndrome
- Oliver–McFarlane syndrome
- Orofaciodigital syndrome
- Pachydermoperiostosis (idiopathic hypertrophic osteoathorpathy, Touraine–Solente–Gole syndrome)
- Peeling skin syndrome (acral peeling skin syndrome, continual peeling skin syndrome, familial continual skin peeling, idiopathic deciduous skin, keratolysis exfoliativa congenita)
- Pfeiffer syndrome
- Photosensitivity–ichthyosis–brittle sulfur-deficient hair–impaired intelligence–decreased fertility–short stature syndrome
- Pityriasis rotunda (pityriasis circinata, tinea circinata)
- Plate-like osteoma cutis
- Plaque-type porokeratosis (classic porokeratosis, porokeratosis of Mibelli)
- Polyneuropathy–organomegaly–endocrinopathy–monoclonal gammopathy–skin changes syndrome (Crow–Fukase syndrome)
- Polyostotic fibrous dysplasia (Albright's disease)
- Popliteal pterygium syndrome
- Porokeratosis
- Porokeratosis palmaris et plantaris disseminata
- Prader–Willi syndrome
- Progeria (Hutchinson–Gilford progeria syndrome, Hutchinson–Gilford syndrome, progeria syndrome)
- Progressive osseous heteroplasia
- Progressive symmetric erythrokeratodermia (erythrokeratodermia progressiva symmetrica)
- Proteus syndrome
- Proteus-like syndrome
- Punctate porokeratosis
- Rapp–Hodgkin syndrome (Rapp–Hodgkin ectodermal dysplasia syndrome)
- Recessive dystrophic epidermolysis bullosa (Hallopeau–Siemens variant of epidermolysis bullosa, Hallopeau–Siemens disease)
- Refsum's disease (heredopathia atactica polyneuritiformis, phytanic acid storage disease)
- Relapsing linear acantholytic dermatosis
- Restrictive dermopathy
X-linked ichthyosis - Rhizomelic chondrodysplasia punctata (autosomal recessive chondrodysplasia punctata type 1, chondrodystrophia calcificans punctata, peroxisomal biogenesis disorder complementation group 11)
- Rombo syndrome
- Rothmund–Thomson syndrome (poikiloderma congenitale)
- Rud syndrome
- Say syndrome
- Scalp–ear–nipple syndrome (Finlay–Marks syndrome)
- Schindler disease (Kanzaki disease, alpha-N-acetylgalactosaminidase deficiency)
- Schinzel–Giedion syndrome
- Scleroatrophic syndrome of Huriez (Huriez syndrome, palmoplantar keratoderma with scleroatrophy, palmoplantar keratoderma with sclerodactyly, scleroatrophic and keratotic dermatosis of the limbs, sclerotylosis)
- Segmental neurofibromatosis
- Senter syndrome (Desmons' syndrome)
- Shabbir syndrome (laryngo–onycho–cutaneous syndrome)
- Silver–Russell syndrome
- Sjögren–Larsson syndrome
- Skin fragility syndrome (plakophilin 1 deficiency)
- Smith–Lemli–Opitz syndrome
- Sturge–Weber syndrome
- Supernumerary nipples–uropathies–Becker's nevus syndrome
- Terminal osseous dysplasia with pigmentary defects
- Tooth and nail syndrome (hypodontia with nail dysgenesis, Witkop syndrome)
- Townes–Brocks syndrome
- Transient bullous dermolysis of the newborn

Xeroderma pigmentosum - Treacher Collins syndrome (Treacher Collins–Franceschetti syndrome)
- Tricho–dento–osseous syndrome
- Tricho–rhino–phalangeal syndrome
- Tuberous sclerosis (Bourneville disease, epiloia)
- Turner syndrome
- Ulnar–mammary syndrome
- Van Der Woude syndrome
- Von Hippel–Lindau syndrome
- Watson syndrome
- Werner syndrome (adult progeria)
- Westerhof syndrome
- Whistling syndrome (craniocarpotarsal syndrome, distal arthrogryposis type 2, Freeman–Sheldon syndrome, Windmill–Vane–Hand syndrome)
- Wilson–Turner syndrome
- Wolf–Hirschhorn syndrome (4p- syndrome)
- X-linked ichthyosis (steroid sulfatase deficiency, X-linked recessive ichthyosis)
- X-linked recessive chondrodysplasia punctata
- Xeroderma pigmentosum (Cockayne syndrome complex)
- XXYY genotype
- Zimmermann–Laband syndrome
Infection-related
Infection-related cutaneous conditions may be caused by bacteria, fungi, yeast, viruses, or parasites.[26][69]
Bacterium-related
Bacterium-related cutaneous conditions often have distinct morphologic characteristics that may be an indication of a generalized systemic process or simply an isolated superficial infection.[69][70]
- Aeromonas infection
- African tick bite fever
- American tick bite fever (Rickettsia parkeri infection)
- Arcanobacterium haemolyticum infection
- Bacillary angiomatosis
- Bejel (endemic syphilis)
- Blastomycosis-like pyoderma (pyoderma vegetans)
- Blistering distal dactylitis
- Botryomycosis
- Brill–Zinsser disease
- Brucellosis (Bang's disease, Malta fever, undulant fever)
- Bubonic plague
- Bullous impetigo
- Cat scratch disease (cat scratch fever, English–Wear infection, inoculation lymphoreticulosis, subacute regional lymphadenitis)
- Cellulitis

Cellulitis - Chancre
- Chancroid (soft chancre, ulcus molle)
- Chlamydial infection
- Chronic lymphangitis
- Chronic recurrent erysipelas
- Chronic undermining burrowing ulcers (Meleney gangrene)
- Chromobacteriosis infection
- Condylomata lata
- Cutaneous actinomycosis
- Cutaneous anthrax infection
- Cutaneous C. diphtheriae infection (Barcoo rot, diphtheric desert sore, septic sore, Veldt sore)
- Cutaneous group B streptococcal infection
- Cutaneous Pasteurella hemolytica infection
- Cutaneous Streptococcus iniae infection
- Dermatitis gangrenosa (gangrene of the skin)
- Ecthyma
- Ecthyma gangrenosum
- Ehrlichiosis ewingii infection
- Elephantiasis nostras
- Endemic typhus (murine typhus)
- Epidemic typhus (epidemic louse-borne typhus)
- Erysipelas (ignis sacer, Saint Anthony's fire)
- Erysipeloid of Rosenbach
- Erythema marginatum
- Erythrasma
- External otitis (otitis externa, swimmer's ear)

External otitis - Felon
- Flea-borne spotted fever
- Flinders Island spotted fever
- Flying squirrel typhus
- Folliculitis
- Fournier gangrene (Fournier gangrene of the penis or scrotum)
- Furunculosis (boil)
- Gas gangrene (clostridial myonecrosis, myonecrosis)
- Glanders (equinia, farcy, malleus)
- Gonococcemia (arthritis–dermatosis syndrome, disseminated gonococcal infection)
- Gonorrhea (clap)
- Gram-negative folliculitis
- Gram-negative toe web infection
- Granuloma inguinale (Donovanosis, granuloma genitoinguinale, granuloma inguinale tropicum, granuloma venereum, granuloma venereum genitoinguinale, lupoid form of groin ulceration, serpiginous ulceration of the groin, ulcerating granuloma of the pudendum, ulcerating sclerosing granuloma)
- Green nail syndrome
- Group JK Corynebacterium sepsis
- Haemophilus influenzae cellulitis
- Helicobacter cellulitis
- Hospital furunculosis
- Hot tub folliculitis (Pseudomonas aeruginosa folliculitis)
- Human granulocytotropic anaplasmosis
- Human monocytotropic ehrlichiosis
- Impetigo contagiosa
- Japanese spotted fever
- Leptospirosis (Fort Bragg fever, pretibial fever, Weil's disease)
- Listeriosis
- Ludwig's angina
- Lupoid sycosis
- Lyme disease (Afzelius' disease, Lyme borreliosis)
- Lymphogranuloma venereum (climatic bubo, Durand–Nicolas–Favre disease, lymphogranuloma inguinale, poradenitis inguinale, strumous bubo)
- Malakoplakia (malacoplakia)
- Mediterranean spotted fever (Boutonneuse fever)
- Melioidosis (Whitmore's disease)
- Meningococcemia
- Missouri Lyme disease
- Mycoplasma infection
- Necrotizing fasciitis (flesh-eating bacteria syndrome)
- Neonatal toxic shock-like exanthematous disease
- Nocardiosis
- Noma neonatorum
- North Asian tick typhus
- Ophthalmia neonatorum
Erysipelas - Oroya fever (Carrion's disease)
- Pasteurellosis
- Perianal cellulitis (perineal dermatitis, streptococcal perianal disease)
- Periapical abscess
- Pinta
- Pitted keratolysis (keratolysis plantare sulcatum, keratoma plantare sulcatum, ringed keratolysis)
- Plague
- Primary gonococcal dermatitis
- Pseudomonal pyoderma
- Pseudomonas hot-foot syndrome
- Pyogenic paronychia
- Pyomyositis
- Q fever
- Queensland tick typhus
- Rat-bite fever
- Recurrent toxin-mediated perineal erythema
- Rhinoscleroma
- Rickettsia aeschlimannii infection
- Rickettsialpox
- Rocky Mountain spotted fever
- Saber shin (anterior tibial bowing)
- Saddle nose
- Salmonellosis
- Scarlet fever
- Scrub typhus (Tsutsugamushi fever)
- Shigellosis
- Staphylococcal scalded skin syndrome (pemphigus neonatorum, Ritter's disease)
- Streptococcal intertrigo
- Superficial pustular folliculitis (impetigo of Bockhart, superficial folliculitis)
- Sycosis vulgaris (barber's itch, sycosis barbae)
- Syphilid
- Syphilis (lues)
- Tick-borne lymphadenopathy
- Toxic shock syndrome (streptococcal toxic shock syndrome, streptococcal toxic shock-like syndrome, toxic streptococcal syndrome)
- Trench fever (five-day fever, quintan fever, urban trench fever)
- Tropical ulcer (Aden ulcer, jungle rot, Malabar ulcer, tropical phagedena)
- Tularemia (deer fly fever, Ohara's disease, Pahvant Valley plague, rabbit fever)
- Verruga peruana
- Vibrio vulnificus infection
- Yaws (bouba, frambösie, parangi, pian)
Mycobacterium-related
Mycobacterium-related cutaneous conditions are caused by Mycobacterium infections.[69][71]
- Aquarium granuloma (fish-tank granuloma, swimming-pool granuloma)
- Borderline lepromatous leprosy
- Borderline leprosy
- Borderline tuberculoid leprosy
- Buruli ulcer (Bairnsdale ulcer, Searl ulcer, Searle's ulcer)

Buruli ulcer - Erythema induratum (Bazin disease)
- Histoid leprosy
- Lepromatous leprosy
- Leprosy (Hansen's disease)
- Lichen scrofulosorum (tuberculosis cutis lichenoides)
- Lupus vulgaris (tuberculosis luposa)
- Miliary tuberculosis (disseminated tuberculosis, tuberculosis cutis acuta generalisata, tuberculosis cutis disseminata)
- Mycobacterium avium-intracellulare complex infection
- Mycobacterium haemophilum infection
- Mycobacterium kansasii infection
- Papulonecrotic tuberculid
- Primary inoculation tuberculosis (cutaneous primary complex, primary tuberculous complex, tuberculous chancre)
- Rapid-growing Mycobacterium infection
- Scrofuloderma (tuberculosis cutis colliquativa)
- Tuberculosis cutis orificialis (acute tuberculous ulcer, orificial tuberculosis)
- Tuberculosis verrucosa cutis (lupus verrucosus, prosector's wart, warty tuberculosis)
- Tuberculous cellulitis
- Tuberculous gumma (metastatic tuberculous abscess, metastatic tuberculous ulcer)
- Tuberculoid leprosy
Mycosis-related
Mycosis-related cutaneous conditions are caused by fungi or yeasts, and may present as either a superficial or deep infection of the skin, hair, or nails.[69]
- African histoplasmosis
- Alternariosis
- Antibiotic candidiasis (iatrogenic candidiasis)
- Black piedra
- Candidal intertrigo
- Candidal onychomycosis
- Candidal paronychia
- Candidal vulvovaginitis
- Candidid
- Chromoblastomycosis (chromomycosis, cladosporiosis, Fonseca's disease, Pedroso's disease, phaeosporotrichosis, verrucous dermatitis)
- Chronic mucocutaneous candidiasis
- Coccidioidomycosis (California disease, desert rheumatism, San Joaquin Valley fever, valley fever)
- Congenital cutaneous candidiasis
- Cryptococcosis
- Dermatophytid
- Diaper candidiasis
- Disseminated coccidioidomycosis (coccidioidal granuloma)
- Distal subungual onychomycosis
- Entomophthoromycosis
- Erosio interdigitalis blastomycetica

Favus - Favus
- Fungal folliculitis (majocchi granuloma)
- Fusariosis
- Geotrichosis
- Granuloma gluteale infantum
- Histoplasmosis (cave disease, Darling's disease, Ohio Valley disease, reticuloendotheliosis)
- Hyalohyphomycosis
- Kerion
- Lobomycosis (keloidal blastomycosis, lacaziosis, Lobo's disease)
- Mucormycosis
- Mycetoma (Madura foot, maduromycosis)
- North American blastomycosis (blastomycetic dermatitis, blastomycosis, Gilchrist's disease)
- Onychomycosis (dermatophytic onychomycosis, ringworm of the nail, tinea unguium)
- Oral candidiasis (thrush)
- Otomycosis
- Perianal candidiasis
- Perlèche (angular cheilitis)
- Phaeohyphomycosis
- Piedra (trichosporosis)
- Pityrosporum folliculitis
- Primary cutaneous aspergillosis
- Primary cutaneous coccidioidomycosis
- Primary cutaneous histoplasmosis
- Primary pulmonary coccidioidomycosis
- Primary pulmonary histoplasmosis
- Progressive disseminated histoplasmosis
- Proximal subungual onychomycosis
- Rhinosporidiosis
- South American blastomycosis (Brazilian blastomycosis, paracoccidioidal granuloma, paracoccidioidomycosis)
- Sporotrichosis (rose-gardener's disease)
- Systemic candidiasis
- Tinea barbae (barber's itch, ringworm of the beard, tinea sycosis)

Tinea barbae - Tinea capitis (herpes tonsurans, ringworm of the hair, ringworm of the scalp, scalp ringworm, tinea tonsurans)
- Tinea corporis (ringworm, tinea circinata, tinea glabrosa)
- Tinea corporis gladiatorum
- Tinea cruris (crotch itch, eczema marginatum, gym itch, jock itch, ringworm of the groin)
- Tinea faciei
- Tinea imbricata (tokelau)
- Tinea incognito
- Tinea manuum
- Tinea nigra (superficial phaeohyphomycosis, tinea nigra palmaris et plantaris)
- Tinea pedis (athlete's foot, ringworm of the foot)
- Tinea versicolor (dermatomycosis furfuracea, pityriasis versicolor, tinea flava)
- Trichophyton mentagrophytes VII (TMVII) (an emerging sexually transmitted tinea of the genitals, buttocks, face, trunk, and extremities)
- White piedra
- White superficial onychomycosis
- Zygomycosis (phycomycosis)
Parasitic infestations, stings, and bites
Parasitic infestations, stings, and bites in humans are caused by several groups of organisms belonging to the following phyla: Annelida, Arthropoda, Bryozoa, Chordata, Cnidaria, Cyanobacteria, Echinodermata, Nemathelminthes, Platyhelminthes, and Protozoa.[69][72]
- Acanthamoeba infection
- Amebiasis cutis
- Ant sting
- Arachnidism
- Baker's itch
- Balamuthia infection
- Bedbug infestation (bedbug bite, cimicosis)
- Bee and wasp stings
- Blister beetle dermatitis
- Bombardier beetle burn
- Bristleworm sting

Creeping eruption - Centipede bite
- Cheyletiella dermatitis
- Chigger bite
- Coolie itch
- Copra itch
- Coral dermatitis
- Creeping eruption (cutaneous larva migrans)
- Cutaneous leishmaniasis (Aleppo boil, Baghdad boil, bay sore, Biskra button, Chiclero ulcer, Delhi boil, Kandahar sore, Lahore sore, leishmaniasis tropica, oriental sore, pian bois, uta)
- Cysticercosis cutis
- Demodex folliculitis, usually caused by the Demodex folliculorum mite
- Dogger Bank itch
- Dracunculiasis (dracontiasis, guinea worm disease, Medina worm)
- Echinococcosis (hydatid disease)
- Elephantiasis tropica (elephantiasis arabum)
- Elephant skin
- Enterobiasis (oxyuriasis, pinworm infection, seatworm infection)
- Erisipela de la costa
- Feather pillow dermatitis
- Funnel web spider bite
- Gamasoidosis
- Gnathostomiasis (larva migrans profundus)
- Grain itch (barley itch, mattress itch, prairie itch, straw itch)
- Grocer's itch
- Head lice infestation (cooties, pediculosis capitis)
- Hookworm disease (ancylostomiasis, ground itch, necatoriasis, uncinariasis)
- Human trypanosomiasis
- Hydroid dermatitis
- Irukandji syndrome
- Jellyfish dermatitis
- Ked itch
- Larva currens
- Latrodectism (widow spider bite)
- Leech bite
- Leopard skin
- Lepidopterism (Caripito itch, caterpillar dermatitis, moth dermatitis)
- Lizard skin
- Loaiasis (Calabar swelling, fugitive swelling, loa loa, tropical swelling)
- Loxoscelism (brown recluse spider bite, necrotic cutaneous loxoscelism)
- Mal morando
- Millipede burn
- Mosquito bite
- Mucocutaneous leishmaniasis (espundia, leishmaniasis Americana)
- Myiasis
- Nairobi fly dermatitis (Kenya fly dermatitis, Nairobi eye)
- Nematode dermatitis
- Norwegian scabies (crusted scabies)

Norwegian scabies - Onchocerciasis
- Ophthalmia nodosa
- Paederus dermatitis
- Pediculosis corporis (pediculosis vestimenti, Vagabond's disease)
- Pediculosis pubis (crabs, phthirus pubis, phthirus pubis, pubic lice)
- Pneumocystosis (often classified as fungal)
- Portuguese man-of-war dermatitis
- Post-kala-azar dermal leishmaniasis (post-kala-azar dermatosis)
- Protothecosis
- Pulicosis (flea bites)
- Reduviid bite
- Scabies (itch mite infestation, seven-year itch)
- Scorpion sting
- Sea anemone dermatitis
- Seabather's eruption (sea lice)
- Sea urchin injury
- Seaweed dermatitis
- Snake bite
- Sowda
- Sparganosis
- Spider bite
- Stingray injury
- Swimmer's itch (cercarial dermatitis, schistosome cercarial dermatitis)

Swimmer's itch - Tarantula bite
- Tick bite
- Toxoplasmosis
- Trichinosis
- Trichomoniasis
- Tungiasis (bicho de pie, chigoe flea bite, jigger bite, nigua, pique)
- Visceral leishmaniasis (dumdum fever, kala-azar)
- Visceral schistosomiasis (bilharziasis)
- Viscerotropic leishmaniasis
- Wheat warehouse itch
Virus-related
Virus-related cutaneous conditions are caused by two main groups of viruses–DNA and RNA types–both of which are obligatoryintracellularparasites.[69][73]
- Alphavirus infection
- Asymmetric periflexural exanthem of childhood (unilateral laterothoracic exanthem)
- B virus infection
- Boston exanthem disease
- Bovine papular stomatitis
- Bowenoid papulosis
- Buffalopox
- Butcher's wart
- Chikungunya fever
- Condylomata acuminata
- Congenital rubella syndrome
- Cowpox
- Cytomegalic inclusion disease
- Dengue (Break-bone fever)
- Disseminated herpes zoster
- Eczema herpeticum (Kaposi's varicelliform eruption)

Eczema vaccinatum - Eczema vaccinatum
- Epidermodysplasia verruciformis
- Eruptive pseudoangiomatosis
- Erythema infectiosum (fifth disease, slapped cheek disease)
- Exanthem of primary HIV infection (acute retroviral syndrome)
- Farmyard pox
- Generalized vaccinia
- Genital herpes (herpes genitalis, herpes progenitalis)
- Gianotti–Crosti syndrome (infantile papular acrodermatitis, papular acrodermatitis of childhood, papulovesicular acrolocated syndrome)
- Giant condyloma acuminatum (Buschke–Löwenstein tumor, giant condyloma of Buschke–Löwenstein tumor)
- Hand-foot-and-mouth disease
- Heck's disease (focal epithelial hyperplasia)
- Hemorrhagic fever with renal syndrome
- Hepatitis B
- Hepatitis C
- Herpangina
- Herpes gladiatorum (scrum pox)
- Herpes simplex
- Herpes zoster oticus (Ramsay–Hunt syndrome)
- Herpetic keratoconjunctivitis
- Herpetic sycosis
- Herpetic whitlow
- HIV-associated pruritus
- Human monkeypox
- Human T-lymphotropic virus 1 infection
- Human tanapox
- Immune reconstitution inflammatory syndrome (immune recovery syndrome)
- Infectious mononucleosis (glandular fever)
- Inflammatory skin lesions following zoster infection (isotopic response)
- Intrauterine herpes simplex

Kaposi sarcoma - Kaposi sarcoma
- Lassa fever
- Lipschütz ulcer (ulcus vulvae acutum)
- Measles (rubeola, morbilli)
- Milker's nodule
- Modified varicella-like syndrome
- Molluscum contagiosum
- Myrmecia
- Neonatal herpes simplex
- Ophthalmic zoster
- Orf (contagious pustular dermatosis, ecthyma contagiosum, infectious labial dermatitis, sheep pox)
- Orf-induced immunobullous disease
- Orolabial herpes (herpes labialis)
- Papular purpuric gloves and socks syndrome
- Pigmented wart
- Postherpetic neuralgia (zoster-associated pain)
- Post-vaccination follicular eruption
- Progressive vaccinia (vaccinia gangrenosum, vaccinia necrosum)
- Pseudocowpox
- Recurrent respiratory papillomatosis (laryngeal papillomatosis)
Varicella - Rift Valley fever
- Roseola infantum (exanthem subitum, exanthema subitum, sixth disease)
- Roseola vaccinia
- Rubella (German measles)
- Sandfly fever (Pappataci fever, phlebotomus fever)
- Sealpox
- Varicella (chickenpox)
- Variola major (smallpox)
- Verruca plana (flat wart)
- Verruca plantaris (plantar wart)
- Verruca vulgaris (wart)
- Verrucae palmares et plantares
- Viral-associated trichodysplasia (ciclosporin-induced folliculodystrophy)
- Wasting syndrome
- West Nile virus infection
- Zoster (herpes zoster, shingles)
- Zoster sine herpete
Lichenoid eruptions
Lichenoid eruptions are dermatoses related to the unique, common inflammatory disorder lichen planus, which affects the skin, mucous membranes, nails, and hair.[74][75][76]
- Annular lichen planus

Lichen planus actinicus - Atrophic lichen planus
- Bullous lichen planus (vesiculobullous lichen planus)
- Erosive lichen planus
- Erythema dyschromicum perstans (ashy dermatosis, dermatosis cinecienta)
- Giant cell lichenoid dermatitis
- Hepatitis-associated lichen planus
- Hypertrophic lichen planus (lichen planus verrucosus)
- Idiopathic eruptive macular pigmentation
- Inverse lichen planus
- Keratosis lichenoides chronica (Nékam's disease)
- Kraurosis vulvae
- Lichen nitidus
- Lichen planus actinicus (actinic lichen nitidus, actinic lichen planus, lichen planus atrophicus annularis, lichen planus subtropicus, lichen planus tropicus, lichenoid melanodermatitis, lichenoid melanodermatosis, summertime actinic lichenoid eruption)
- Lichen planus pemphigoides
- Lichen planus pigmentosus
- Lichen planus–lichen sclerosus overlap syndrome
- Lichen ruber moniliformis
- Lichen sclerosus (lichen sclerosus et atrophicus)
- Lichen striatus (Blaschko linear acquired inflammatory skin eruption, linear lichenoid dermatosis)
- Lichen verrucosus et reticularis
- Lichenoid trikeratosis
- Lichenoid dermatitis
- Lichenoid reaction of graft-versus-host disease
- Linear lichen planus
- Mucosal lichen planus
- Peno-gingival syndrome
- Ulcerative lichen planus
- Vulvovaginal gingival syndrome
- Vulvovaginal lichen planus
Lymphoid-related
Lymphoid-related cutaneous conditions are a group of disorders characterized by collections of lymphocyte cells within the skin.[77]
- Adult T-cell leukemia/lymphoma
- Angiocentric lymphoma (extranodal natural killer cell lymphoma, nasal-type NK lymphoma, NK/T-cell lymphoma, polymorphic/malignant midline reticulosis)
- Angioimmunoblastic T-cell lymphoma (angioimmunoblastic lymphadenopathy with dysproteinemia)
- Blastic NK-cell lymphoma
- CD30+ cutaneous T-cell lymphoma (primary cutaneous anaplastic large cell lymphoma)
- Cutaneous lymphoid hyperplasia (borrelial lymphocytoma, lymphadenosis benigna cutis, lymphocytoma cutis, pseudolymphoma, pseudolymphoma of Spiegler and Fendt, sarcoidosis of Spiegler and Fendt, Spiegler–Fendt lymphoid hyperplasia, Spiegler–Fendt sarcoid)

Cutaneous lymphoid hyperplasia - Cutaneous lymphoid hyperplasia with bandlike and perivascular patterns
- Cutaneous lymphoid hyperplasia with nodular pattern (nodular pattern of cutaneous lymphoid hyperplasia)
- Diffuse large B-cell lymphoma (primary cutaneous large B-cell lymphoma)
- Granulocytic sarcoma (chloroma, myeloid sarcoma)
- Granulomatous slack skin
- Hairy-cell leukemia
- Hodgkin's disease
- Ichthyosis acquisita (acquired ichthyosis)
- IgG4-related skin disease
- Intravascular large B-cell lymphoma (angiotropic large cell lymphoma, intralymphatic lymphomatosis, intravascular lymphomatosis, malignant angioendotheliomatosis)
- Jessner lymphocytic infiltrate of the skin (benign lymphocytic infiltration of the skin, Jessner lymphocytic infiltration of the skin, Jessner–Kanof lymphocytic infiltration of the skin, lymphocytic infiltrate of Jessner)
- Kikuchi's disease (histiocytic necrotizing lymphadenitis)
- Large plaque parapsoriasis (parapsoriasis en plaques)
- Lennert lymphoma (lymphoepitheliod lymphoma)
- Leukemia cutis
- Lymphoma cutis
- Lymphomatoid granulomatosis
- Lymphomatoid papulosis
- Malignant histiocytosis (histiocytic medullary reticulosis)
- Marginal zone B-cell lymphoma
- Mucosa-associated lymphoid tissue lymphoma
- Mycosis fungoides
- Non-mycosis fungoides CD30− cutaneous large T-cell lymphoma
- Nonspecific cutaneous conditions associated with leukemia (leukemid)
- Pagetoid reticulosis (acral mycoses fungoides, localized epidermotropic reticulosis, mycosis fungoides palmaris et plantaris, unilesional mycosis fungoides, Woringer–Kolopp disease)
- Pityriasis lichenoides chronica (chronic guttate parapsoriasis, chronic pityriasis lichenoides, dermatitis psoriasiformis nodularis, parapsoriasis chronica, parapsoriasis lichenoides chronica)
- Pityriasis lichenoides et varioliformis acuta (acute guttate parapsoriasis, acute parapsoriasis, acute pityriasis lichenoides, Mucha–Habermann disease, parapsoriasis acuta, parapsoriasis lichenoides et varioliformis acuta, parapsoriasis varioliformis)
- Plasmacytoma

Mycosis fungoides - Plasmacytosis
- Pleomorphic T-cell lymphoma (non-mycosis fungoides CD30− pleomorphic small/medium-sized cutaneous T-cell lymphoma)
- Polycythemia vera (erythremia)
- Primary cutaneous follicular lymphoma (follicular center cell lymphoma, follicular center lymphoma)
- Primary cutaneous immunocytoma
- Primary cutaneous marginal zone lymphoma
- Retiform parapsoriasis
- Secondary cutaneous CD30+ large cell lymphoma
- Sézary syndrome
- Sinus histiocytosis with massive lymphadenopathy (Rosai–Dorfman disease)
- Subcutaneous T-cell lymphoma (panniculitis-like T-cell lymphoma)
- Vesiculopustular eruption and leukemoid reaction in Down syndrome
Melanocytic nevi and neoplasms
Melanocytic nevi and neoplasms are caused by either a proliferation of (1) melanocytes, or (2) nevus cells, a form of melanocyte that lack dendritic processes.[78][79]
- Acral nevus (melanocytic nevus of acral skin, melanocytic nevus with intraepidermal ascent of cells)
- Amelanotic blue nevus (hypomelanotic blue nevus)

Becker's nevus - Balloon cell nevus
- Bannayan–Riley–Ruvalcaba syndrome
- Becker's nevus (Becker's melanosis, Becker's pigmentary hamartoma, nevoid melanosis, pigmented hairy epidermal nevus)
- Benign melanocytic nevus (banal nevus, common acquired melanocytic nevus, mole, nevocellular nevus, nevocytic nevus)
- Blue nevus (blue neuronevus, dermal melanocytoma, nevus bleu)
- Blue nevus of Jadassohn–Tièche (common blue nevus, nevus ceruleus)
- Carney complex (LAMB syndrome, NAME syndrome)
- Cellular blue nevus
- Centrofacial lentiginosis
- Congenital melanocytic nevus
- Deep penetrating nevus
- Dysplastic nevus (atypical mole, atypical nevus, B-K mole, Clark's nevus, dysplastic melanocytic nevus, nevus with architectural disorder)
- Dysplastic nevus syndrome (B-K mole syndrome, familial atypical multiple mole–melanoma syndrome, familial melanoma syndrome)
- Ephelis (freckle)
- Epithelioid blue nevus
- Generalized lentiginosis
- Giant pigmented nevus (bathing trunk nevus, congenital nevomelanocytic nevus, garment nevus, giant hairy nevus, nevus pigmentosus et pilosus)
- Halo nevus (leukoderma acquisitum centrifugum, perinevoid vitiligo, Sutton nevus)
- Hori's nevus (acquired bilateral nevus of Ota-like macules)
- Inherited patterned lentiginosis in black persons
- Ink spot lentigo (sunburn lentigo)
- Laugier–Hunziker syndrome
- Lentigo simplex (simple lentigo)
- Malignant blue nevus
- Medium-sized congenital nevocytic nevus
- Melanoacanthoma
- Melanocytic tumors of uncertain malignant potential
- Moynahan syndrome
- Mucosal lentigines (labial and penile and vulvar melanosis, melanotic macules)
- Nevus of Ito (nevus fuscoceruleus acromiodeltoideus)
- Nevus of Ota (congenital melanosis bulbi, melanosis bulborum and aberrant dermal melanocytosis, nevus fuscoceruleus ophthalmomaxillaris, oculodermal melanocytosis, oculomucodermal melanocytosis)
- Nevus spilus (speckled lentiginous nevus, zosteriform lentiginous nevus)
- Partial unilateral lentiginosis (segmental lentiginosis)
- Peutz–Jeghers syndrome
- Pigmented spindle cell nevus (pigmented spindle cell tumor of Reed, pigmented variant of Spitz nevus)
- Pseudomelanoma (recurrent melanocytic nevus, recurrent nevus)
- PUVA lentigines
- Small-sized congenital nevocytic nevus
- Spitz nevus (benign juvenile melanoma, epithelioid and spindle cell nevus, Spitz's juvenile melanoma)
- Solar lentigo (lentigo senilis, liver spot, old age spot, senile freckle)
Melanoma
Melanoma is a malignant proliferation of melanocytes and the most aggressive type of skin cancer.[80][81][82]
- Acral lentiginous melanoma

Nodular melanoma - Amelanotic melanoma
- Animal-type melanoma
- Desmoplastic melanoma (neurotropic melanoma, spindled melanoma)
- Lentigo maligna (lentiginous melanoma on sun-damaged skin)
- Lentigo maligna melanoma
- Melanoma with features of a Spitz nevus (Spitzoid melanoma)
- Melanoma with small nevus-like cells (small cell melanoma)
- Mucosal melanoma
- Nevoid melanoma
- Nodular melanoma
- Polypoid melanoma
- Seborrheic keratosis-like melanoma
- Soft-tissue melanoma (clear-cell sarcoma, melanoma of the soft parts)
- Superficial spreading melanoma (superficially spreading melanoma)
- Uveal melanoma
Monocyte- and macrophage-related
Monocyte- and macrophage-related cutaneous conditions are characterized histologically by infiltration of the skin by monocyte or macrophage cells,[10] often divided into several categories, including granulomatous disease,[83]histiocytoses,[84] and sarcoidosis.[85]
- Actinic granuloma (O'Brien granuloma)
- Annular elastolytic giant cell granuloma (giant cell elastophagocytosis, Meischer's granuloma, Miescher's granuloma of the face)
- Annular sarcoidosis
Generalized granuloma annulare - Benign cephalic histiocytosis (histiocytosis with intracytoplasmic worm-like bodies)
- Congenital self-healing reticulohistiocytosis (Hashimoto–Pritzker disease, Hashimoto–Pritzker syndrome)
- Erythrodermic sarcoidosis
- Generalized eruptive histiocytoma (eruptive histiocytoma, generalized eruptive histiocytosis)
- Generalized granuloma annulare
- Giant cell reticulohistiocytoma (solitary reticulohistiocytoma, solitary reticulohistiocytosis)
- Granuloma annulare in HIV disease
- Granuloma multiforme (Mkar disease, granuloma multiforme (Leiker))
- Hand–Schüller–Christian disease
- Heerfordt's syndrome
- Hereditary progressive mucinous histiocytosis
- Hypopigmented sarcoidosis
- Ichthyosiform sarcoidosis
- Indeterminate cell histiocytosis
- Interstitial granulomatous drug reaction
- Langerhans cell histiocytosis (histiocytosis X)
- Letterer–Siwe disease
- Localized granuloma annulare
- Löfgren syndrome
- Lupus pernio
- Morpheaform sarcoidosis
- Mucosal sarcoidosis
- Multicentric reticulohistiocytosis
- Necrobiotic xanthogranuloma (necrobiotic xanthogranuloma with paraproteinemia)
- Non-X histiocytosis
- Papular sarcoid
- Papular xanthoma
- Patch-type granuloma annulare (macular granuloma annulare)
- Perforating granuloma annulare
Systemic sarcoidosis - Progressive nodular histiocytosis
- Reticulohistiocytoma
- Scar sarcoid (sarcoidosis in scars)
- Sea-blue histiocytosis
- Subcutaneous granuloma annulare (deep granuloma annulare, pseudorheumatoid nodule)
- Subcutaneous sarcoidosis (Darier–Roussy disease, Darier–Roussy sarcoid)
- Systemic sarcoidosis
- Ulcerative sarcoidosis
- Xanthoma disseminatum (disseminated xanthosiderohistiocytosis, Montgomery syndrome)
Mucinoses
Mucinoses are a group of conditions caused by dermalfibroblasts producing abnormally large amounts of mucopolysaccharides.[34]
- Acral persistent papular mucinosis
- Atypical lichen myxedematosus (intermediate lichen myxedematosus)
- Atypical tuberous myxedema (Jadassohn–Dosseker syndrome)
- Cutaneous focal mucinosis
- Cutaneous lupus mucinosis (papular and nodular mucinosis in lupus erythematosus, papular and nodular mucinosis of Gold, papulonodular mucinosis in lupus erythematosus)
- Discrete papular lichen myxedematosus
- Eccrine mucinosis
- Follicular mucinosis (alopecia mucinosa, mucinosis follicularis, Pinkus' follicular mucinosis, Pinkus' follicular mucinosis–benign primary form)
- Localized lichen myxedematosus
- Myxoid cyst (digital mucous cyst, mucous cyst)
- Myxoid lipoblastoma
- Neuropathia mucinosa cutanea
- Nodular lichen myxedematosus
- Papular mucinosis (generalized lichen myxedematosus, sclerodermoid lichen myxedematosus, scleromyxedema)
- Papular mucinosis of infancy (cutaneous mucinosis of infancy)
- Perifollicular mucinosis
- Reticular erythematous mucinosis (midline mucinosis, plaque-like cutaneous mucinosis, REM syndrome)
- Scleroderma
- Self-healing juvenile cutaneous mucinosis
- Self-healing papular mucinosis
- Stiff skin syndrome (congenital fascial dystrophy)
Neurocutaneous
Neurocutaneous conditions are due organicnervous system disease or are psychiatric in etiology.[86][87]
- Atypical chronic pain syndrome
- Body dysmorphic disorder (dysmorphic syndrome, dysmorphophobia)
- Brachioradial pruritus
- Bromidrosiphobia
- Complex regional pain syndrome (reflex sympathetic dystrophy)
- Congenital insensitivity to pain with anhidrosis
- Delusional parasitosis (delusions of parasitosis, Ekbom syndrome, monosymptomatic hypochondriacal psychosis)
- Dermatothlasia
- Dermatitis artefacta (factitious dermatitis, factitial dermatitis)

Factitious dermatitis - Glossodynia (burning mouth syndrome, burning tongue, orodynia)
- Levator ani syndrome
- Malum perforans pedis (neurotrophic ulcer, perforating ulcer of the foot)
- Meralgia paresthetica (Roth–Bernhardt disease)
- Neurotic excoriations
- Notalgia paresthetica (hereditary localized pruritus, posterior pigmented pruritic patch, subscapular pruritus)
- Postencephalitic trophic ulcer
- Psychogenic pruritus
- Riley–Day syndrome (familial dysautonomia)
- Scalp dysesthesia
- Sciatic nerve injury
- Scrotodynia
- Syringomyelia (Morvan's disease)
- Traumatic neuroma (amputation neuroma)
- Trichotillomania (trichotillosis)
- Trigeminal neuralgia (tic douloureux)
- Trigeminal trophic lesion (trigeminal trophic syndrome)
- Vulvodynia (vestibulodynia)
Noninfectious immunodeficiency-related
Noninfectious immunodeficiency-related cutaneous conditions are caused by T-cell or B-cell dysfunction.[88][89]
- Bare lymphocyte syndrome
- Chronic granulomatous disease (Bridges–Good syndrome, chronic granulomatous disorder, Quie syndrome)
- Common variable immunodeficiency (acquired hypogammaglobulinemia)
- Complement deficiency
- DiGeorge syndrome (DiGeorge anomaly, thymic hypoplasia)
- Graft-versus-host disease
- Griscelli syndrome
- Hyper-IgE syndrome (Buckley syndrome, Job syndrome)
- Immunodeficiency with hyper-IgM
- Immunodeficiency–centromeric instability–facial anomalies syndrome (ICF syndrome)
- Isolated IgA deficiency
- Isolated primary IgM deficiency
- Janus kinase 3 deficiency
- Leukocyte adhesion molecule deficiency
- LIG4 syndrome
- Myeloperoxidase deficiency
- Neutrophil immunodeficiency syndrome
- Nezelof syndrome (thymic dysplasia with normal immunoglobulins)
- Omenn syndrome

Omenn syndrome - Purine nucleoside phosphorylase deficiency
- Severe combined immunodeficiency (alymphocytosis, Glanzmann–Riniker syndrome, severe mixed immunodeficiency syndrome, thymic alymphoplasia)
- Shwachman–Bodian–Diamond syndrome
- Thymoma with immunodeficiency (Good syndrome)
- Transient hypogammaglobulinemia of infancy
- Warts–hypogammaglobulinemia–infections–myelokathexis syndrome (WHIM syndrome)
- Wiskott–Aldrich syndrome
- X-linked agammaglobulinemia (Bruton syndrome, sex-linked agammaglobulinemia)
- X-linked hyper-IgM syndrome
- X-linked hypogammaglobulinemia
- X-linked lymphoproliferative disease (Duncan's disease)
- X-linked neutropenia
Nutrition-related
Nutrition-related cutaneous conditions are caused by malnutrition due to an improper or inadequate diet.[90][91]
- Biotin deficiency
- Carotenemia
- Essential fatty acid deficiency
- Folic acid deficiency
- Hypervitaminosis A
- Hypovitaminosis A (phrynoderma)
- Iron deficiency

Kwashiorkor - Kwashiorkor
- Lycopenemia
- Maple syrup urine disease
- Marasmus
- Niacin deficiency (pellagra, vitamin B3 deficiency)
- Selenium deficiency
- Vitamin B1 deficiency (beriberi, thiamine deficiency)
- Vitamin B12 deficiency (cyanocobalamin deficiency)
- Vitamin B2 deficiency (ariboflavinosis, riboflavin deficiency)
- Vitamin B6 deficiency (pyridoxine deficiency)
- Vitamin B6 excess (pyridoxine excess)
- Vitamin C deficiency (scurvy)
- Vitamin K deficiency
- Zinc deficiency
Papulosquamous hyperkeratotic
Papulosquamoushyperkeratotic cutaneous conditions are those that present with papules and scales caused by a thickening of the stratum corneum.[9]

- Confluent and reticulated papillomatosis (confluent and reticulated papillomatosis of Gougerot and Carteaud, familial cutaneous papillomatosis, familial occurrence of confluent and reticulated papillomatosis)
- Digitate dermatosis
- Drug-induced keratoderma
- Exfoliative dermatitis (dermatitis exfoliativa, erythroderma, red man syndrome)
- Florid cutaneous papillomatosis
- Granular parakeratosis (axillary granular parakeratosis, intertriginous granular parakeratosis)
- Keratolysis exfoliativa (lamellar dyshidrosis, recurrent focal palmar peeling, recurrent palmar peeling)
- Keratosis punctata of the palmar creases (hyperkeratosis penetrans, hyperkeratosis punctata, keratodermia punctata, keratosis punctata, keratotic pits of the palmar creases, lenticular atrophia of the palmar creases, punctate keratosis of the palmar creases)
- Meesmann corneal dystrophy
- Paraneoplastic keratoderma
- Pityriasis rosea (pityriasis rosea Gibert)
- Pityriasis rubra pilaris (Devergie's disease, lichen ruber acuminatus, lichen ruber pilaris)
- Pure hair-nail type ectodermal dysplasia
- Small plaque parapsoriasis (chronic superficial dermatitis)
- Tripe palms
- Xanthoerythrodermia perstans
Palmoplantar keratodermas
Palmoplantar keratodermas are a diverse group of hereditary and acquired keratodermas in which there is hyperkeratosis of the skin of the palms and soles.[92]

- Acrokeratoelastoidosis of Costa (keratoelastoidosis marginalis)
- Aquagenic keratoderma (acquired aquagenic palmoplantar keratoderma, aquagenic syringeal acrokeratoderma, aquagenic wrinkling of the palms, transient reactive papulotranslucent acrokeratoderma)
- Bart–Pumphrey syndrome (palmoplantar keratoderma with knuckle pads and leukonychia and deafness)
- Camisa disease
- Carvajal syndrome (striate palmoplantar keratoderma with woolly hair and cardiomyopathy, striate palmoplantar keratoderma with woolly hair and left ventricular dilated cardiomyopathy)
- Corneodermatoosseous syndrome (CDO syndrome)
- Diffuse epidermolytic palmoplantar keratoderma (palmoplantar keratoderma cum degeneratione granulosa Vörner, Vörner's epidermolytic palmoplantar keratoderma, Vörner keratoderma)
- Diffuse nonepidermolytic palmoplantar keratoderma (diffuse orthohyperkeratotic keratoderma, hereditary palmoplantar keratoderma, keratosis extremitatum progrediens, keratosis palmoplantaris diffusa circumscripta, tylosis, Unna–Thost disease, Unna–Thost keratoderma)
- Erythrokeratodermia variabilis (erythrokeratodermia figurata variabilis, keratosis extremitatum progrediens, keratosis palmoplantaris transgrediens et progrediens, Mendes da Costa syndrome, Mendes da Costa type erythrokeratodermia, progressive symmetric erythrokeratoderma)
- Focal acral hyperkeratosis (acrokeratoelastoidosis lichenoides, degenerative collagenous plaques of the hand)
- Focal palmoplantar and gingival keratosis
- Focal palmoplantar keratoderma with oral mucosal hyperkeratosis (focal epidermolytic palmoplantar keratoderma, hereditary painful callosities, hereditary painful callosity syndrome, keratosis follicularis, keratosis palmoplantaris nummularis, nummular epidermolytic palmoplantar keratoderma)
- Haim–Munk syndrome (palmoplantar keratoderma with periodontitis and arachnodactyly and acro-osteolysis)
- Hidrotic ectodermal dysplasia (alopecia congenita with keratosis palmoplantaris, Clouston syndrome, Clouston's hidrotic ectodermal dysplasia, Fischer–Jacobsen–Clouston syndrome, keratosis palmaris with drumstick fingers, palmoplantar keratoderma and clubbing)
- Howel–Evans syndrome (familial keratoderma with carcinoma of the esophagus, focal non-epidermolytic palmoplantar keratoderma with carcinoma of the esophagus, palmoplantar ectodermal dysplasia type III, palmoplantar keratoderma associated with esophageal cancer, tylosis, tylosis–esophageal carcinoma)
- Hystrix-like ichthyosis–deafness syndrome (HID syndrome)
- Keratoderma climactericum (acquired plantar keratoderma, climacteric keratoderma, Haxthausen's disease)
- Keratosis punctata palmaris et plantaris (Buschke–Fischer–Brauer disease, Davis Colley disease, keratoderma disseminatum palmaris et plantaris, keratosis papulosa, keratoderma punctatum, keratodermia punctata, keratoma hereditarium dissipatum palmare et plantare, palmar and plantar seed dermatoses, palmar keratoses, papulotranslucent acrokeratoderma, punctate keratoderma, punctate keratoses of the palms and soles, maculosa disseminata)
- Keratitis–ichthyosis–deafness syndrome (erythrokeratodermia progressiva Burns, ichthyosiform erythroderma with corneal involvement and deafness, KID syndrome)
- Mal de Meleda (acral keratoderma, Gamborg–Nielsen keratoderma, mutilating palmoplantar keratoderma of the Gamborg–Nielsen type, palmoplantar ectodermal dysplasia type VIII, palmoplantar keratoderma of the Norrbotten type)
- Naxos syndrome (diffuse non-epidermolytic palmoplantar keratoderma with woolly hair and cardiomyopathy, diffuse palmoplantar keratoderma with woolly hair and arrythmogenic right ventricular cardiomyopathy of Naxos, Naxos disease)
- Olmsted syndrome (mutilating palmoplantar keratoderma with periorificial keratotic plaques, mutilating palmoplantar keratoderma with periorificial plaques, polykeratosis of Touraine)
- Pachyonychia congenita type I (Jadassohn–Lewandowsky syndrome)
- Pachyonychia congenita type II (Jackson–Lawler pachyonychia congenita, Jackson–Sertoli syndrome)
- Palmoplantar keratoderma and spastic paraplegia (Charcot–Marie–Tooth disease with palmoplantar keratoderma and nail dystrophy)
- Palmoplantar keratoderma of Sybert (Greither palmoplantar keratoderma, Greither syndrome, keratosis extremitatum hereditaria progrediens, keratosis palmoplantaris transgrediens et progrediens, Sybert keratoderma, transgrediens and progrediens palmoplantar keratoderma)
- Papillon–Lefèvre syndrome (palmoplantar keratoderma with periodontitis)
- Porokeratosis plantaris discreta
- Punctate palmoplantar keratoderma
- Schöpf–Schulz–Passarge syndrome (eyelid cysts with palmoplantar keratoderma and hypodontia and hypotrichosis)
- Scleroatrophic syndrome of Huriez (Huriez syndrome, palmoplantar keratoderma with scleroatrophy, palmoplantar keratoderma with sclerodactyly, scleroatrophic and keratotic dermatosis of the limbs, sclerotylosis)
- Striate palmoplantar keratoderma (acral keratoderma, Brünauer–Fuhs–Siemens type of palmoplantar keratoderma, focal non-epidermolytic palmoplantar keratoderma, keratosis palmoplantaris varians, palmoplantar keratoderma areata, palmoplantar keratoderma striata, Wachter keratoderma, Wachters palmoplantar keratoderma)
- Spiny keratoderma (porokeratosis punctata palmaris et plantaris, punctate keratoderma, punctate porokeratosis of the palms and soles)
- Tyrosinemia type II (oculocutaneous tyrosinemia, Richner–Hanhart syndrome)
- Vohwinkel syndrome (keratoderma hereditaria mutilans, keratoma hereditaria mutilans, mutilating keratoderma of Vohwinkel, mutilating palmoplantar keratoderma)
Pregnancy-related

Pregnancy-related cutaneous conditions are a group of skin changes observed during pregnancy.[93][94]
- Impetigo herpetiformis
- Intrahepatic cholestasis of pregnancy (cholestasis of pregnancy, jaundice of pregnancy, obstetric cholestasis, prurigo gravidarum)
- Linea nigra
- Pemphigoid gestationis (gestational pemphigoid, herpes gestationis)
- Prurigo gestationis (Besnier prurigo, early-onset prurigo of pregnancy, linear IgM dermatosis of pregnancy, papular dermatitis of pregnancy, prurigo of pregnancy, Spangler's papular dermatitis of pregnancy)
- Pruritic folliculitis of pregnancy
- Pruritic urticarial papules and plaques of pregnancy (late-onset prurigo of pregnancy, polymorphic eruption of pregnancy, PUPPP syndrome, toxemic rash of pregnancy, toxic erythema of pregnancy)
- Striae gravidarum
Pruritic
Pruritus, commonly known as itchiness, is a sensation exclusive to the skin, and characteristic of many skin conditions.[95][96]
- Adult blaschkitis
- Aquadynia
- Aquagenic pruritus
- Biliary pruritus
- Cholestatic pruritus
- Drug-induced pruritus
- Hydroxyethyl starch-induced pruritus
- Lichen simplex chronicus (neurodermatitis)

Lichen simplex chronicus - Prion pruritus
- Prurigo nodularis
- Prurigo pigmentosa
- Prurigo simplex
- Pruritus ani
- Pruritus scroti
- Pruritus vulvae
- Puncta pruritica (itchy points)
- Scalp pruritus
- Senile pruritus
- Uremic pruritus (renal pruritus)
Psoriasis
Psoriasis is a common, chronic, and recurrent inflammatory disease of the skin characterized by circumscribed, erythematous, dry, scaling plaques.[97][98][99]

- Annular pustular psoriasis
- Drug-induced psoriasis
- Exanthematic pustular psoriasis
- Generalized pustular psoriasis (pustular psoriasis of von Zumbusch)
- Guttate psoriasis (eruptive psoriasis)
- Inverse psoriasis
- Keratoderma blennorrhagica (keratoderma blennorrhagicum)
- Localized pustular psoriasis
- Napkin psoriasis
- Psoriasis vulgaris (chronic stationary psoriasis, plaque-like psoriasis)
- Psoriatic arthritis
- Psoriatic erythroderma (erythrodermic psoriasis)
- Seborrheic-like psoriasis (sebopsoriasis, seborrhiasis)
Reactive neutrophilic
Reactive neutrophilic cutaneous conditions constitute a spectrum of disease mediated by neutrophils, and typically associated with underlying diseases, such as inflammatory bowel disease and hematologicmalignancy.[100][101]

- Acute erythema nodosum
- Bowel-associated dermatosis–arthritis syndrome (bowel bypass syndrome, bowel bypass syndrome without bowel bypass, intestinal bypass arthritis–dermatitis syndrome)
- Marshall syndrome
- Neutrophilic dermatosis of the dorsal hands (pustular vasculitis of the dorsal hands)
- Neutrophilic eccrine hidradenitis
- Pyoderma gangrenosum
- Pyogenic arthritis–pyoderma gangrenosum–acne syndrome (PAPA syndrome)
- Rheumatoid neutrophilic dermatitis (rheumatoid neutrophilic dermatosis)
- Superficial granulomatous pyoderma
- Sweet's syndrome (acute febrile neutrophilic dermatosis)
- Sweet's syndrome-like dermatosis
- Vesicopustular dermatosis
Recalcitrant palmoplantar eruptions
Recalcitrant palmoplantar eruptions are skin conditions of the palms and soles which are resistant to treatment.[34]
- Dermatitis repens (acrodermatitis continua, acrodermatitis continua of Hallopeau, acrodermatitis continua suppurativa Hallopeau, acrodermatitis perstans, dermatitis repens Crocker, Hallopeau's acrodermatitis, Hallopeau's acrodermatitis continua, pustular acrodermatitis)
- Infantile acropustulosis (acropustulosis of infancy)
- Palmoplantar pustulosis (persistent palmoplantar pustulosis, pustular psoriasis of the Barber type, pustular psoriasis of the extremities, pustulosis of palms and soles, pustulosis palmaris et plantaris)
- Pustular bacterid
Resulting from errors in metabolism
Skin conditions resulting from errors in metabolism are caused by enzymatic defects that lead to an accumulation or deficiency of various cellular components, including, but not limited to, amino acids, carbohydrates, and lipids.[16]
- Acute intermittent porphyria
- Adrenoleukodystrophy (Schilder's disease)
- Alkaptonuria
- Aminolevulinic acid dehydratase deficiency porphyria (Doss porphyria, plumboporphyria)
- B-mannosidase deficiency
- Carotenosis
- Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy syndrome (CADASIL syndrome)
- Cerebrotendinous xanthomatosis
- Citrullinemia
- Congenital erythropoietic porphyria (Gunther's disease)
- Diabetic bulla (bullosis diabeticorum, bullous eruption of diabetes mellitus)
- Diabetic cheiroarthropathy
- Diabetic dermopathy (shin spots)
- Dystrophic calcinosis cutis
- Eruptive xanthoma
- Erythropoietic protoporphyria

Erythropoietic protoporphyria - Fabry disease (Anderson–Fabry disease, angiokeratoma corporis diffusum)
- Familial alpha-lipoprotein deficiency (Tangier disease)
- Familial amyloid polyneuropathy
- Familial apoprotein CII deficiency
- Familial combined hyperlipidemia (multiple-type hyperlipoproteinemia)
- Familial defective apolipoprotein B-100
- Familial dysbetalipoproteinemia (broad beta disease, remnant removal disease)
- Familial hypertriglyceridemia
- Farber disease (fibrocytic dysmucopolysaccharidosis, lipogranulomatosis)
- Fucosidosis
- Gaucher's disease
- Gout (podagra, urate crystal arthropathy, urate deposition disease)
- Hartnup disease (pellagra-like dermatosis)
- Hemodialysis-associated amyloidosis
- Hepatoerythropoietic porphyria
- Hereditary coproporphyria
- Hereditary gelsolin amyloidosis
- Heredofamilial amyloidosis
- Hunter syndrome
- Hurler syndrome (gargoylism, mucopolysaccharidosis type I)
- Hurler–Scheie syndrome (mucopolysaccharidosis type I H-S)
- Hyaluronidase deficiency (mucopolysaccharidosis type IX)
- Iatrogenic calcinosis cutis
- Idiopathic scrotal calcinosis (idiopathic calcified nodules of the scrotum)
- Lafora disease
- Lesch–Nyhan syndrome (juvenile gout)
- Lichen amyloidosis
- Limited joint mobility
- Lipoid proteinosis (hyalinosis cutis et mucosae, Urbach–Wiethe disease)
- Lipoprotein lipase deficiency (chylomicronemia, chylomicronemia syndrome)
- Macular amyloidosis

Xanthoma tendinosum - Maroteaux–Lamy syndrome (mucopolysaccharidosis type VI)
- Medication-induced hyperlipoproteinemia
- Metastatic calcinosis cutis
- Milia-like calcinosis
- Morquio's disease (mucopolysaccharidosis type IV)
- Necrobiosis lipoidica (necrobiosis lipoidica diabeticorum)
- Niemann–Pick disease
- Nodular amyloidosis
- Nodular xanthoma
- Normolipoproteinemic xanthomatosis
- Obstructive liver disease (xanthomatous biliary cirrhosis)
- Ochronosis
- Osteoma cutis
- Palmar xanthoma
- Phenylketonuria
- Phytosterolemia (sitosterolemia)
- Porphyria cutanea tarda
- Primary cutaneous amyloidosis
- Primary systemic amyloidosis
- Prolidase deficiency
- Pseudoporphyria (pseudoporphyria cutanea tarda)
- Sanfilippo syndrome
- Scheie syndrome (mucopolysaccharidosis type I S)
- Secondary cutaneous amyloidosis
- Secondary systemic amyloidosis
- Sialidosis
- Sly syndrome (mucopolysaccharidosis type VII)
- Subepidermal calcified nodule (solitary congenital nodular calcification, Winer's nodular calcinosis)
- Transient erythroporphyria of infancy (purpuric phototherapy-induced eruption)

Xanthelasma palpebrarum - Traumatic calcinosis cutis
- Tuberoeruptive xanthoma (tuberous xanthoma)
- Tumoral calcinosis
- Variegate porphyria (mixed hepatic porphyria, mixed porphyria, South African genetic porphyria, South African porphyria)
- Verruciform xanthoma
- Waxy skin
- Wilson's disease (hepatolenticular degeneration)
- Xanthelasma palpebrarum (xanthelasma)
- Xanthoma diabeticorum
- Xanthoma planum (plane xanthoma)
- Xanthoma striatum palmare
- Xanthoma tendinosum (tendinous xanthoma)
- Xanthoma tuberosum
Resulting from physical factors
Skin conditions resulting from physical factors occur from a number of causes, including, but not limited to, hot and cold temperatures, friction, and moisture.[34][102][103]
- Abrasion
- Acrocyanosis
- Actinic prurigo (familial polymorphous light eruption of American Indians, hereditary polymorphous light eruption of American Indians, Hutchinson's summer prurigo, hydroa aestivale)
- Aerosol burn
- Benign summer light eruption
- Beryllium granuloma
- Black heel and palm (black heel, calcaneal petechiae, chromidrose plantaire, post-traumatic punctate intraepidermal hemorrhage, tache noir)
- Callus (callosity, clavus, corn, heloma, heloma durum, heloma molle, intractable plantar keratosis, tyloma)
- Carbon stain

Chilblains - Chilblains (pernio, perniosis)
- Chronic actinic dermatitis (actinic reticuloid, chronic photosensitivity dermatitis, persistent light reactivity, photosensitive eczema)
- Colloid milium
- Coma blister
- Delayed blister
- Dermatosis neglecta
- Edema blister (edema bulla, hydrostatic bulla, stasis blister)
- Electrical burn
- Equestrian perniosis
- Erythema ab igne (fire stains, toasted skin syndrome)
- Erythrocyanosis crurum
- Favre–Racouchot syndrome (Favre–Racouchot disease, nodular cutaneous elastosis with cysts and comedones)
- Foreign body reaction
- Fracture blister
- Friction blister
- Frostbite
- Garrod's pad (violinist's pad)
- Harpist's finger
- Heel stick wound
- Heat edema
- Hot tar burn
- Hunan hand syndrome (chili burn)
- Hydroa vacciniforme (Bazin's hydroa vacciniforme)
- Jogger's nipple
- Juvenile spring eruption
- Kairo cancer
- Kang cancer
- Kangri ulcer
- Lightning burn
- Loop mark
- Magnetic resonance imaging burn (MRI burn)
- Mercury granuloma
- Miliaria crystallina (miliaria crystalline, sudamina)
- Miliaria profunda (mammillaria)
- Miliaria pustulosa
- Miliaria rubra (heat rash, prickly heat)
- Narcotic dermopathy
- Occlusion miliaria
- Painful fat herniation (painful piezogenic pedal papules, piezogenic papules)
- Peat fire cancer
- Photoaging (dermatoheliosis)
- Photosensitivity with HIV infection
- Phototoxic tar dermatitis
- Photosenitization
- Phytophotodermatitis (Berloque dermatitis)
- Pinch mark
- Polymorphous light eruption (polymorphic light eruption)
- Postmiliarial hypohidrosis
Pressure ulcer - Postoperative hematoma
- Pressure ulcer (decubitus ulcer)
- Pseudoacanthosis nigricans
- Pseudoverrucous papules and nodules
- Pulling boat hands
- PUVA-induced acrobullous dermatosis
- Runner's rump
- Sclerosing lymphangiitis
- Silica granuloma
- Silicone granuloma
- Skin pop scar
- Skin track
- Slap mark
- Solar erythema
- Soot tattoo
- Subcutaneous emphysema
- Sucking blister
- Sunburn
- Surfer's knots
- Talon noir
- Tattoo
- Tennis toe
- Thermal burn
- Traumatic asphyxia
- Trench foot
- Tropical anhidrotic asthenia
- Tropical immersion foot (paddy foot, paddy-field foot)
- Turf toe
- Uranium dermatosis
- UV-sensitive syndrome
- Vibration white finger (dead finger, hand–arm vibration syndrome)
- Warm water immersion foot
- Weathering nodule of ear
- Wrestler's ear (cauliflower ear, traumatic auricular hematoma)
- Zirconium granuloma
Ionizing radiation-induced
Ionizing radiation-induced cutaneous conditions result from exposure to ionizing radiation.[104]
- Acute radiodermatitis

Fluoroscopy burn - Chronic radiation keratosis
- Chronic radiodermatitis
- Eosinophilic, polymorphic, and pruritic eruption associated with radiotherapy
- Fluoroscopy burn
- Radiation acne
- Radiation cancer
- Radiation dermatitis (radiodermatitis)
- Radiation recall reaction
- Radiation-induced erythema multiforme
- Radiation-induced hypertrophic scar
- Radiation-induced keloid
- Radiation-induced morphea
Urticaria and angioedema
Urticaria is a vascular reaction of the skin characterized by the appearance of wheals, which are firm, elevated swellings of the skin.[105]Angioedema, which can occur alone or with urticaria, is characterized by a well-defined, edematous swelling that involves subcutaneous tissues, abdominal organs, or upper airway.[106]
- Acquired C1 esterase inhibitor deficiency
- Acute urticaria
- Adrenergic urticaria
- Anaphylaxis
- Aquagenic urticaria
- Autoimmune urticaria
- Cholinergic urticaria
- Chronic urticaria (ordinary urticaria)
- Cold urticaria
- Dermatographism (dermographism)
- Episodic angioedema with eosinophilia (Gleich's syndrome)
- Exercise urticaria (exercise-induced urticaria)
- Galvanic urticaria
- Heat urticaria
- Hereditary angioedema (Quincke's edema)
- Localized heat contact urticaria
- Mast cell-independent urticaria
- Physical urticaria
- Primary cold contact urticaria
- Pressure urticaria (delayed pressure urticaria)
- Reflex cold urticaria
- Schnitzler syndrome
- Secondary cold contact urticaria
- Solar urticaria
- Systemic capillary leak syndrome
- Urticarial allergic eruption
- Urticaria-like follicular mucinosis
- Vibratory angioedema
Vascular-related
Vascular-related cutaneous conditions result from dysfunction of the blood or blood vessels in the dermis, or lymphatics in the subcutaneous tissues.[9][107][108]
- Aagenaes syndrome
- Acroangiodermatitis (acroangiodermatitis of Mali, Mali acroangiodermatitis, Pseudo-Kaposi's sarcoma)
- Acrocyanosis
- Acute hemorrhagic edema of infancy (acute hemorrhagic edema of childhood, Finkelstein's disease, infantile postinfectious iris-like purpura and edema, medallion-like purpura, purpura en cocarde avec oedema, Seidlmayer syndrome)
- Arterial insufficiency ulcer (ischemic ulcer)
- Arteriosclerosis obliterans
- Bier spots
- Blueberry muffin baby
- Bonnet–Dechaume–Blanc syndrome (Wyburn–Mason syndrome)
- Bullous lymphedema
- Bullous small vessel vasculitis (bullous variant of small vessel vasculitis)
- Calciphylaxis

Calciphylaxis - Caput succedaneum
- Cholesterol embolus (warfarin blue toe syndrome)
- Cobb syndrome
- Corona phlebectatica
- Cryofibrinogenemic purpura
- Cryoglobulinemic purpura
- Cryoglobulinemic vasculitis
- Cutaneous small-vessel vasculitis (cutaneous leukocytoclastic angiitis, cutaneous leukocytoclastic vasculitis, cutaneous necrotizing venulitis, hypersensitivity angiitis)
- Deep venous thrombosis
- Disseminated intravascular coagulation
- Doucas and Kapetanakis pigmented purpura
- Drug-induced purpura
- Drug-induced thrombocytopenic purpura
- Eczematid-like purpura of Doucas and Kapetanakis
- Epidemic dropsy
- Erythema elevatum diutinum
- Erythromelalgia (acromelalgia, erythermalgia)
- Factitial lymphedema (hysterical edema)
- Fibrinolysis syndrome (defibrinating syndrome, hypofibrinogenemia)
- Food-induced purpura
- Generalized essential telangiectasia (general essential telangiectasia)
- Giant-cell arteritis
- Gougerot–Blum syndrome (pigmented purpuric lichenoid dermatitis, pigmented purpuric lichenoid dermatitis of Gougerot and Blum)
- Granulomatosis with polyangiitis
- Harlequin color change
- Hematopoietic ulcer
- Hennekam syndrome (Hennekam lymphangiectasia-lymphedema syndrome, intestinal lymphagiectasia-lymphedema-mental retardation syndrome)
- Henoch–Schönlein purpura (anaphylactoid purpura, purpura rheumatica, Schönlein–Henoch purpura)

Henoch–Schönlein purpura - Hereditary hemorrhagic telangiectasia (Osler's disease, Osler–Weber–Rendu disease)
- Idiopathic thrombocytopenic purpura (autoimmune thrombocytopenic purpura, Werlhof's disease)
- IgA vasculitis
- Kawasaki's disease (mucocutaneous lymph node syndrome)
- Levamisole-induced vasculitis
- Lichen aureus (lichen purpuricus)
- Livedo racemosa
- Livedo reticularis
- Livedoid dermatitis (embolia cutis medicamentosa, Nicolau syndrome)
- Livedoid vasculopathy (atrophie blanche, livedo reticularis with summer ulceration, livedoid vasculitis, PURPLE syndrome, segmental hyalinizing vasculitis)
- Lymphedema praecox
- Lymphedema–distichiasis syndrome
- Maffucci syndrome
- Majocchi's disease (purpura annularis telangiectodes, purpura annularis telangiectodes of Majocchi)
- Malignant atrophic papulosis (Degos' disease)
- Marshall–White syndrome
- Meige lymphedema
- Microscopic polyangiitis (microscopic polyarteritis, microscopic polyarteritis nodosa)
- Mondor's disease (Mondor's syndrome of superficial thrombophlebitis)
- Neuropathic ulcer (mal perforans)
- Njolstad syndrome
- Nonne–Milroy–Meige syndrome (hereditary lymphedema, Milroy disease)
- Obstructive purpura
- Orthostatic purpura (stasis purpura)
- Painful bruising syndrome (autoerythrocyte sensitization, Gardner–Diamond syndrome, psychogenic purpura)
- Parkes Weber syndrome
- Paroxysmal hand hematoma (Achenbach syndrome)
- Paroxysmal nocturnal hemoglobinuria
- Polyarteritis nodosa (panarteritis nodosa, periarteritis nodosa)
- Postcardiotomy syndrome
- Perinatal gangrene of the buttock
- Pigmentary purpuric eruptions (progressive pigmentary dermatosis, progressive pigmenting purpura, purpura pigmentosa chronica)
- Postinflammatory lymphedema
- Postmastectomy lymphangiosarcoma (Stewart–Treves syndrome)
- Purpura fulminans (purpura gangrenosa)
- Purpura secondary to clotting disorders
- Purpuric agave dermatitis

Raynaud phenomenon - Raynaud phenomenon
- Raynaud's disease (primary Raynaud's phenomenon)
- Reactive angioendotheliomatosis
- Schamberg's disease (progressive pigmentary dermatosis of Schamberg, purpura pigmentosa progressiva, Schamberg's purpura)
- Secondary lymphedema
- Septic thrombophlebitis
- Sinusoidal hemangioma
- Sneddon's syndrome (idiopathic livedo reticularis with cerebrovascular accidents)
- Solar purpura (actinic purpura, senile purpura)
- Stasis dermatitis (congestion eczema, gravitational dermatitis, gravitational eczema, stasis eczema, varicose eczema)
- Superficial thrombophlebitis
- Takayasu arteritis (aortic arch syndrome, pulseless disease)
- Temporal arteritis (cranial arteritis, Horton's disease)
- Thromboangiitis obliterans (Buerger's disease)
- Thrombotic thrombocytopenic purpura (Moschcowitz syndrome)
- Traumatic purpura
- Trousseau's syndrome
- Unilateral nevoid telangiectasia (nevoid telangiectasia)
- Urticarial vasculitis (chronic urticaria as a manifestation of venulitis, hypocomplementemic urticarial vasculitis syndrome, hypocomplementemic vasculitis, unusual lupus-like syndrome)
- Venous insufficiency ulceration
- Waldenström hyperglobulinemic purpura (purpura hyperglobulinemica)
- Waldenström macroglobulinemia
- Yellow nail syndrome (primary lymphedema associated with yellow nails and pleural effusion)
See also
- Category:Cutaneous conditions
- Dermatology
- List of conditions associated with café au lait macules
- List of contact allergens
- List of cutaneous conditions associated with increased risk of nonmelanoma skin cancer
- List of cutaneous conditions associated with internal malignancy
- List of cutaneous conditions caused by mutations in keratins
- List of cutaneous neoplasms associated with systemic syndromes
- List of cutaneous conditions caused by problems with junctional proteins
- List of dental abnormalities associated with cutaneous conditions
- List of genes mutated in cutaneous conditions
- List of genes mutated in pigmented cutaneous lesions
- List of histologic stains that aid in diagnosis of cutaneous conditions
- List of human leukocyte antigen alleles associated with cutaneous conditions
- List of immunofluorescence findings for autoimmune bullous conditions
- List of inclusion bodies that aid in diagnosis of cutaneous conditions
- List of keratins expressed in the human integumentary system
- List of migrating cutaneous conditions
- List of mites associated with cutaneous reactions
- List of radiographic findings associated with cutaneous conditions
- List of specialized glands within the human integumentary system
- List of spiders associated with cutaneous reactions
- List of target antigens in pemphigoid
- List of target antigens in pemphigus
- List of verrucous carcinoma subtypes
- List of xanthoma variants associated with hyperlipoproteinemia subtypes
Footnotes
- ↑Any given cutaneous condition is only included once within this list.
- ↑Parentheticals are used to indicate other names by which a condition is known. If there are multiple alternative names for a condition, they are separated by commas within the parenthetical.
- ↑Citations for any given condition name and/or alternative name(s) may be found within the condition's respective article.
- ↑This list uses American English; therefore, the symbols æ and œ, which are common to British English, are not used, but, rather, simplified to a single e. For example, the spelling of nevus is favored over nævus, edema over œdema, and so forth. For more information, see American and British English differences.
- ↑Non-English names are included within this list when those terms are found in English medical literature. Inclusion of acne excoriée des jeunes filles (French), Frambösie (German), and parangi (Malay) represent examples of this convention.
- ↑Abbreviations for condition names commonly described in medical literature with an acronym or initialism are included within this list.
- ↑Within this list, the term immunoglobulin is abbreviated to Ig when used as a prefix to a specific antibody isotype (i.e. IgA, IgD, IgE, IgG, and IgM).
- ↑Within this list, the terms human immunodeficiency virus and acquired immunodeficiency syndrome are abbreviated to HIV and AIDS, respectively.
References
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- ↑Lippens S, Hoste E, Vandenabeele P, Agostinis P, Declercq W (April 2009). "Cell death in the skin". Apoptosis. 14 (4): 549–69. doi:10.1007/s10495-009-0324-z. PMID 19221876. S2CID 13058619.
- 1234Burns, Tony; et al. (2006) Rook's Textbook of Dermatology CD-ROM. Wiley-Blackwell. ISBN 1-4051-3130-6.
- ↑Paus R, Cotsarelis G (1999). "The biology of hair follicles". N Engl J Med. 341 (7): 491–7. doi:10.1056/NEJM199908123410706. PMID 10441606. S2CID 35532108.
- ↑Goldsmith, Lowell A. (1983). Biochemistry and physiology of the skin. Oxford University Press. ISBN 978-0-19-261253-3.
- ↑Fuchs E (February 2007). "Scratching the surface of skin development". Nature. 445 (7130): 834–42. Bibcode:2007Natur.445..834F. doi:10.1038/nature05659. PMC 2405926. PMID 17314969.
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- 12345Freedberg, Irwin M; et al. (2003). Fitzpatrick's Dermatology in General Medicine. McGraw-Hill. ISBN 978-0-07-138076-8.
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- ↑Lambert WC, Everett MA (October 1981). "The nosology of parapsoriasis". J. Am. Acad. Dermatol. 5 (4): 373–95. doi:10.1016/S0190-9622(81)70100-2. PMID 7026622.
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- ↑Weedon's Skin Pathology, 2-Volume Set: Expert Consult - Online and Print. Edinburgh: Churchill Livingstone. 2009. ISBN 978-0-7020-3941-6.
- 12345David J DiCaudo; Dirk Elston MD; Dirk M Elston; Tammie Ferringer; Christine J Ko; Christine Ko MD; Steven Peckham; Whitney A High (2009). Dermatopathology. Philadelphia: Saunders. ISBN 978-0-7020-3023-9.
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- ↑Fietta P (2004). "Autoinflammatory diseases: the hereditary periodic fever syndromes". Acta Biomed. 75 (2): 92–9. PMID 15481697.
- ↑Centola M, Aksentijevich I, Kastner DL (1998). "The hereditary periodic fever syndromes: molecular analysis of a new family of inflammatory diseases". Hum Mol Genet. 7 (10): 1581–8. doi:10.1093/hmg/7.10.1581. PMID 9735379.
- ↑Chan, Lawrence S (30 March 2009). Blistering Skin Diseases (1 ed.). Manson Publishing Ltd. ISBN 978-1-84076-066-8.
- ↑Yeh SW, Ahmed B, Sami N, Razzaque Ahmed A (2003). "Blistering disorders: diagnosis and treatment". Dermatol Ther. 16 (3): 214–23. doi:10.1046/j.1529-8019.2003.01631.x. PMID 14510878.
- ↑Eming R, Hertl M (2006). "Autoimmune bullous disorders". Clin Chem Lab Med. 44 (2): 144–9. doi:10.1515/CCLM.2006.027. PMID 16475898. S2CID 24967692.
- 1234James, William D; et al. (2006). Andrews' Diseases of the Skin: Clinical Dermatology. Saunders Elsevier. ISBN 978-0-7216-2921-6.
- 12345Christine J Ko; Schwarzenberger, Kathryn; Werchniak, Andrew E (2009). General dermatology. Philadelphia: Saunders. ISBN 978-0-7020-3093-2.
- ↑Aronson IK, Tharp MD (2010). "Diagnosis and Treatment of Panniculitis". Dermatologic Therapy. 23 (4): 317–434. doi:10.1111/j.1529-8019.2010.01331.x. ISSN 1529-8019. PMID 20666818. S2CID 221647926.
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- ↑Requena L, Sánchez Yus E (2001). "Panniculitis. Part II. Mostly lobular panniculitis". J Am Acad Dermatol. 45 (3): 325–61, quiz 362–64. doi:10.1067/mjd.2001.114735. PMID 11511831. S2CID 4824297.
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- ↑Andrea L. Zaenglein; MD, Howard Gimbel; Albert C Yan (2008). Pediatric Dermatology: Requisites in Dermatology. Saunders Ltd. ISBN 978-0-7020-3022-2.
- ↑Cheng, Mao-Jie; Chen, Wen-Chieh; Happle, Rudolf; Song, Zhi-Qiang (8 May 2014). "Familial Disseminated Comedones without Dyskeratosis: Report of an Affected Family and Review of the Literature". Dermatology. 228 (4): 303–306. doi:10.1159/000360818. PMID 24819025– via Silverchair.
- ↑Crofford, Leslie J; Klippel, John H; Weyand, Cornelia M; Stone, John F (2001). Primer on the rheumatic diseases. Atlanta, GA: Arthritis Foundation. ISBN 978-0-912423-29-6.
- ↑Ushiki T (2002). "Collagen fibers, reticular fibers and elastic fibers. A comprehensive understanding from a morphological viewpoint". Arch Histol Cytol. 65 (2): 109–26. doi:10.1679/aohc.65.109. PMID 12164335.
- ↑Alsaad KO, Ghazarian D (2005). "My approach to superficial inflammatory dermatoses". J Clin Pathol. 58 (12): 1233–41. doi:10.1136/jcp.2005.027151. PMC 1770784. PMID 16311340.
- ↑Wüthrich B, Cozzio A, Roll A, Senti G, Kündig T, Schmid-Grendelmeier P (2007). "Atopic eczema: genetics or environment?". Ann Agric Environ Med. 14 (2): 195–201. PMID 18247450.
- ↑Roosterman D, Goerge T, Schneider SW, Bunnett NW, Steinhoff M (2006). "Neuronal control of skin function: the skin as a neuroimmunoendocrine organ". Physiol Rev. 86 (4): 1309–79. doi:10.1152/physrev.00026.2005. PMID 17015491. S2CID 23288191.
- ↑Spergel JM (August 2010). "From atopic dermatitis to asthma: the atopic march". Ann. Allergy Asthma Immunol. 105 (2): 99–106, quiz 107–9, 117. doi:10.1016/j.anai.2009.10.002. PMID 20674819.
- ↑Saint-Mezard P, Rosieres A, Krasteva M, et al. (2004). "Allergic contact dermatitis". Eur J Dermatol. 14 (5): 284–95. PMID 15358566.
- ↑Krasteva M, Kehren J, Sayag M, et al. (1999). "Contact dermatitis II. Clinical aspects and diagnosis". Eur J Dermatol. 9 (2): 144–59. PMID 10066966.
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{{cite journal}}: CS1 maint: DOI inactive as of July 2025 (link) - ↑Steinhoff M, Bienenstock J, Schmelz M, Maurer M, Wei E, Bíró T (2006). "Neurophysiological, neuroimmunological, and neuroendocrine basis of pruritus". J Invest Dermatol. 126 (8): 1705–18. doi:10.1038/sj.jid.5700231. hdl:2437/112565. PMID 16845410.
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Enlaces externos
- Imágenes en dermatología clínica en el New England Journal of Medicine
- afecciones cutáneas
- Listas relacionadas con la dermatología
- Listas de enfermedades

